Chondroid syringoma: an unusual presentation in a 7-year-old boy

Abstract

Coined in 1961 by Hirsch and Helwig, the term chondroid syringoma refers to a rare mixed tumour of subcutaneous tissue. Histologically, these tumours are almost identical to pleomorphic adenomas, arising from salivary glands. With the obvious difference being the presence of sweat gland tissue (syringoma) within a matrix of cartilage (chondroid). These mixed tumours remain scarce throughout the world, with an incidence of less than 0.098%. The vast majority of cases are reported in middle-aged and older adults, where they typically present as painless swellings in the head and neck, which gradually grow in size.

Chondroid syringoma: unusual presentation of a rare tumor

“…3 Tipicamente, manifesta-se como nódulo subcutâneo bem definido, firme, móvel e assintomático, de crescimento lento, medindo de 0,5 a 3cm. 1,3,4 As localizações mais comuns são nariz, lábio superior, couro cabeludo, fronte, mento e região malar. 2 Ainda não está descrito padrão dermatoscópico específico.…”