Chondroid Chordoma in an Atypical Location

Crespo, Iñigo.; Andrés, Juan José Rivas de; Flor, Raúl Embún; Franco, Severiano Cortés

doi:10.1016/j.arbr.2013.09.003

Cited by 4 publications

(6 citation statements)

References 8 publications

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“…Chordoma represents 1-4% of primary malignant bone tumors [1]. It is predominantly male (sex ratio M/F: 2.7/1-1.6/1) [3]. Chordoma is mainly found in the sacrococcygeal and spheno-occipital region, and is rare in the axial skeleton (0.8 to 1/100,000 persons/year) [4,5].…”

Section: Discussionmentioning

confidence: 99%

“…The clinical manifestations of chordoma are locationdependent, with symptoms secondary to compression and invasion of the surrounding organs. In the dorsal spine, patients may present chest pain, dyspnea, and spinal pain, especially if the tumor is large [3,7].…”

Section: Discussionmentioning

confidence: 99%

“…Magnetic resonance imaging is more sensitive than CT to assess extension into the epidural and intradural space, especially to look for spinal cord compression, epidural metastases, or epiduritis [3].…”

Section: Discussionmentioning

confidence: 99%

“…The 5-year survival rate of chondroid chordoma is generally between 10% and 70% [3]. Only 10-20% of chordoma are curable by surgery with a local recurrence rate between 26% and 68% [3]. Adjuvant radiotherapy is often used to improve local control [5].…”

Section: Discussionmentioning

confidence: 99%

“…Chordoma is a very rare, insidious, locally invasive, malignant primary bone tumor that develops in exceptional cases from the embryonic remnants of the notochord of the axial skeleton [1][2][3]. Chondroid chordoma is a rare histological variant of chordoma, it is characterized by the presence of a cartilaginous matrix, and it has a better prognosis compared to the classical chordoma [2].…”

Section: Introductionmentioning

confidence: 99%

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Chondroid chordoma within dorsal spine

Jihane¹,

Nabil²,

Nassar³

2022

Int J Case Rep Images

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Introduction:Chordoma is an extremely rare malignant bone tumor that mainly affects the sacrococcygeal and spheno-occipital regions. Localization in the spine is exceptional and occurs mainly in young individuals.Case Report: We report the case of a 32-year-old male patient with a chondroid chordoma in the dorsal spine which is a very rare histological subtype of chordoma. Conclusion:The chondroid chordoma is an uncommon malignant bone tumor. An intrathoracic chordoma manifesting as a posterior mediastinal tumor is unusual, it appears especially in young individuals. The imaging helps to allow a better characterization of the tumor.

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Section: Discussionmentioning

confidence: 99%

Section: Discussionmentioning

confidence: 99%

Section: Discussionmentioning

confidence: 99%

Section: Discussionmentioning

confidence: 99%

Section: Introductionmentioning

confidence: 99%

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Chondroid chordoma within dorsal spine

Jihane¹,

Nabil²,

Nassar³

2022

Int J Case Rep Images

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Unusual Presentation of Thoracic Chordoma with Spinal Epidural Hematoma: A Rare Case Report and PRISMA-Driven Systematic Review

Abualkhair,

Sharif,

Eid

et al. 2024

Clin Med Insights Case Rep

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A chordoma is a slow growing, locally invasive, low-grade tumor belonging to the sarcoma family. It mainly affects the sacrum and skull base. We present a case of thoracic chordoma initially presented with epidural hematoma (EDH), which is a rare clinical entity. We reported this case, and also performed a PRISMA-driven systematic review to summary the similar cases in the literature. This review includes the clinical characteristics and outcome of thoracic chordoma. Our case involves a 60-year-old male who, despite no history of trauma, presented with acute paraparesis. An epidural hematoma was identified at T6 level, leading to a surgical intervention involving T4-6 laminectomy and fixation. Six months subsequent to surgery, the patient experienced progressive lower limb weakness and spasticity. Computed tomography (CT) exhibited erosion of T6 and an associated aggressive mass. Magnetic resonance imaging (MRI) revealed a large heterogenous soft tissue mass arising from the vertebral body and right pedicle of D6, protruding in the epidural space and compressing the spinal cord focally at this level. The mass measured approximately 5 × 4 × 3.5 cm. Magnetic resonance myelography indicated a filling defect at T5–6 level, confirming the intraspinal location of the soft tissue lesion. Complete excision of the mass confirmed the diagnosis of thoracic chordoma. Postoperative follow-up demonstrated notable improvement in the lower limb spasticity and paraparesis, and the patient started adjuvant radiotherapy. This case underscores the importance of maintaining a high index of suspicion when evaluating presentations resembling EDH.

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Chondroid chordoma- A rare tumor diagnosed on cytology: A case report

Singh¹,

Sangma²,

Singh³

et al. 2020

IJPO

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Chordomas are rare, malignant and locally aggressive tumors that are derived from the remnants of primitive notochord, out of which chondroid chordomas are even rarer. Very few case reports have described this variant, which is difficult to pick up on cytopathology alone and has a number of other differentials too. We report here a case of chondroid chordoma at the sacrococcygeal region that was diagnosed on FNAC in an elderly male patient emphasizing on its cytomorphology and how to differentiate from its cytological mimickers.

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Chondroid Chordoma in an Atypical Location

Cited by 4 publications

References 8 publications

Chondroid chordoma within dorsal spine

Chondroid chordoma within dorsal spine

Unusual Presentation of Thoracic Chordoma with Spinal Epidural Hematoma: A Rare Case Report and PRISMA-Driven Systematic Review

Chondroid chordoma- A rare tumor diagnosed on cytology: A case report

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