Anomalous left coronary artery from the pulmonary artery is a rare congenital heart disease, which is the main cause of myocardial ischemia and severe left ventricular dysfunction in children, leading to an increase in the size of the left ventricle, a decrease in the left ventricular ejection fraction and secondary mitral regurgitation.The aim. To evaluate the preoperative characteristics of patients with anomalous left coronary artery from the pulmonary artery, immediate and long-term results after surgical correction of the defect.Object and research methods. From 2008 to 2024, 20 patients with anomalous coronary artery from the pulmonary artery were surgically corrected at the National Amosov Institute of Cardiovascular Surgery of the National Academy of Medical Sciences of Ukraine. The median age at the time of surgery was 32 [2; 564] months. The median left ventricular ejection fraction before surgical correction was 55 [17; 73] %. In 15 (75%) patients, there were concomitant congenital heart disease in combination with anomalous left coronary artery from the pulmonary artery.Results of the study. Hospital mortality in the early postoperative period was 5% (1 patient). An uncomplicated course of the early postoperative period was observed in 15 (75%) patients. The median LVEF at the time of discharge from the hospital was 57 [39; 70] %. In 6 (30%) patients, moderate mitral insufficiency persisted after surgery. In the long-term period, 1 (5%) patient underwent repeated surgical intervention.Conclusions. Anomalous left coronary artery abduction from the pulmonary artery is a rare congenital heart disease, which is one of the most common causes of ischemia and myocardial infarction, so surgical correction in childhood can prevent the development of irreversible complications.