Cervical ecchordosis physaliphora: CT and MR features.

Sh, Ng; Ko, Sheung‐Fat; Wan, Yung‐Liang; Tang, Lei; Ho, Yat Sen

doi:10.1259/bjr.71.843.9616246

Cited by 37 publications

(18 citation statements)

References 6 publications

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“…2,6,21,23,24,26,27,37 These histological qualities lend to their iso-to hypointensity on T1-weighted MRI and hyperintensity on T2-weighted MRI. 6,22,23,34,35 However, EP demonstrates no contrast enhancement, unlike chordomas, which usually enhance and are more often located extradurally. 3,21,35 These are helpful features in making the distinction between the two lesions.…”

Section: Discussionmentioning

confidence: 99%

Giant ecchordosis physaliphora in an adolescent girl

Krisht

Palmer²,

Osborn

et al. 2013

PED

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The authors describe a rare case of giant ecchordosis physaliphora (EP) in a 16-year-old female patient who presented with diplopia. Magnetic resonance imaging of the brain with Gd contrast revealed a 3.0 × 1.7 × 1.8–cm nonenhancing, extraaxial epidural mass along the dorsal aspect of the clivus that was T2 hyperintense and T1 isointense with intermediate signal on diffusion sequences. Resection via a transnasal transsphenoidal approach to the ventral clival wall resulted in a stable tumor size with no evidence of interval growth after 30 months. Although this case features a strictly extradural EP, this tumor more commonly occurs in the subdural space and requires differentiation from intradural chordoma. Unlike EP, intradural chordoma may enhance with Gd contrast, is more likely to be associated with cranial nerve palsies and brainstem symptoms, and will occasionally have an elevated MIB-1 index. In this paper the authors highlight the different possible midline locations for both EP and chordoma, the difficulty in distinguishing between intradural giant EP and intradural chordoma, and the potential occurrence of these lesions in young people despite their typically slow rate of growth, while also underscoring the need for further investigation into the tumors' cytogenetic behavior.

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Section: Discussionmentioning

confidence: 99%

Giant ecchordosis physaliphora in an adolescent girl

Krisht

Palmer²,

Osborn

et al. 2013

PED

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“…They are often located intracranially, on the dorsum of the clivus and in the prepontine cisterna [13]. They can be found at any level from the dorsum sellae to the saccrococcygeal region and are usually present extradurally [13]. Ecchordoses grow slowly and in most cases are clinically asymptomatic [7].…”

Section: Discussionmentioning

confidence: 99%

“…Ecchordoses grow slowly and in most cases are clinically asymptomatic [7]. Some rare cases do become symptomatic trough tumour expansion, brain compression or haemorrhage [13]. Because of their location, the differential diagnosis with BNCTs is easy [1].…”

Section: Discussionmentioning

confidence: 99%

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Case Report: An Unusual Osseous Lesion

Rivière¹,

Rousset²,

Bauchet³

et al. 2013

OJPathology

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The intraosseous benign notochordal cell tumor (BNCT) is an intravertebral lesion derived from notochordal tissue. The notochord develops in humans during the third week of embryonic life and persists in adults as the nucleus pulposus of the vertebral disks. The most common locations of such tumors are the saccrococcygeal region and the skull base. Most tumors are asymptomatic and small. Magnetic resonance imaging is useful in their detection and precise localization. Histologically, these lesions consist of sheets of adipocyte-like vacuolated or less vacuolated eosinophilic tumor cells with eccentrically located round nuclei without myxoid matrix. The tumor cells express the epithelial markers, vimentin and S100 protein. Main differential diagnosis is chordoma. Intraosseous BNCT do not require any surgical management and should be recognized by pathologists to prevent unnecessary radical surgery. These lesions should be followed-up with conventional MRI.

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“…The frequency of this finding varies between 0.5 and 2% of autopsies [8]. EP is usually asymptomatic and only few authors have reported EP-associated symptoms due to tumour expansion and compression of the surrounding structures [1,12,13].…”

Section: Introductionmentioning

confidence: 99%

Sudden death due to subarachnoid bleeding from ecchordosis physaliphora

2007

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Ecchordosis physaliphora (EP) is a rare intracranial mass derived from ectopic notochordal tissue. It is usually a fortuitous finding at autopsy or by computed tomography/magnetic resonance imaging. Very few authors have described an EP-associated symptomatology. In this study, we report a case of the sudden and unexpected death of a 48-year-old woman. At autopsy, the cause of death was subarachnoid bleeding, the origin of which was identified as a gelatinous mass stemming from the dura mater and occupying the prepontine space. Further histological and immunohistochemical investigations allowed the diagnosis of EP.

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Cervical ecchordosis physaliphora: CT and MR features.

Cited by 37 publications

References 6 publications

Giant ecchordosis physaliphora in an adolescent girl

Giant ecchordosis physaliphora in an adolescent girl

Case Report: An Unusual Osseous Lesion

Sudden death due to subarachnoid bleeding from ecchordosis physaliphora

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