Cerebrovascular Moyamoya disease.

Effect of Moyamoya Disease on Neuropsychological Functioning in Adults

“…Despite some early interest (11), there has been little neuropsychological research on moyamoya disease in adults. The adult literature is composed of five case studies (3,11,14,18,21).…”

“…The adult literature is composed of five case studies (3,11,14,18,21). The results of presurgical neuropsychological testing in these cases indicate that impairment in intellect (18), speed of information processing (3), executive functioning (18), and visual spatial ability (11,14,21) can occur. In this small series of cases, the most consistent finding was relatively intact memory functioning (3,18,21).…”

Moya-moya disease: clinical and pathological report of a case with associated myopathy.

“…The condition is also recognised as occurring infrequently in the UK although no published details of incidence are available. Indeed the disease is sufficiently uncommon outside Japan among Caucasians and Negroes that reports describe small numbers of cases or even single patients (Simon et al, 1968;Busch, 1969;Lepoire et al, 1969;Galligioni et al, 1971;O'Sullivan, 1973;Hoare and Keogh, 1974;Poor and Gacs, 1974;Sogaard and Jorgensen, 1975;Meriwether et al, H. B. Coakham, L. W. Duchen, and F. Scaravilli and symptoms of spatial disorientation, being unable to dress himself and losing his way in familiar surroundings. Over the previous four years he had developed progressive weakness of the proximal lower limb muscles, with symptoms including difficulty in rising from low chairs.…”

“…The condition is also recognised as occurring infrequently in the UK although no published details of incidence are available. Indeed the disease is sufficiently uncommon outside Japan among Caucasians and Negroes that reports describe small numbers of cases or even single patients (Simon et al, 1968;Busch, 1969;Lepoire et al, 1969;Galligioni et al, 1971;O'Sullivan, 1973;Hoare and Keogh, 1974;Poor and Gacs, 1974;Sogaard and Jorgensen, 1975;Meriwether et al, Accepted 2 October 19781976). This contrasts with the Japanese experience as illustrated by a series of 376 cases (see Kudo, 1971).…”

The Role of SPECT and MRI for Pre and Postoperative Evaluation of Childhood Moyamoya Disease: Case Report and Review of Literature

“…It was later reported by Nishimoto and Takeuchi in 1968 [8] and was reported by Hoare et al in a western journal in 1974 [9]. Nishimoto et al also described a remarkable angiographic appearance seen in Japanese children [8].…”