“…Noninfectious aortitis is a rare but clinically significant disease which appears to have a higher incidence in the second or third decade of life in individuals of Indian, Japanese, Southeast Asian, and South African descent. 2,3 Aortitis has been increasingly reported across the world resulting from a variety of etiologies further sub-classified into infectious and noninfectious sources. 1 Examples of non-infectious etiologies include giant cell arteritis (GCA), Takayasu arteritis, IGG4-related disease, idiopathic retroperitoneal fibrosis, spondyloarthropathies, reactive arthritis, rheumatoid arthritis, systemic lupus erythematosus, Behcet's disease, granulomatosis with polyangiitis, polyarteritis nodosa, sarcoidosis, and inflammatory aortic aneurysm.…”