Case Report of Symptomatic and Asymptomatic Ebstein’s AnomalyCardiac MR Imaging

Right Heart Failure Indicative of Ebstein’s Disease in Adulthood about a Case

“…Ebstein's disease is a congenital anomaly of the tricuspid valve whose septal and posterior leaflets are attached to the ventricular wall and moved to the tip of the right ventricle [6]. These anatomical abnormalities divide the right ventricle into a thin-walled proximal portion that atrial and widens, and a more distal trabeculate component that forms the functional right ventricle [7]. The pathophysiological consequences of this malformation are tricuspid insufficiency, intra-atrial mechanical desynchronization by sequential activation of the true atrial segment and the atrial ventricular segment and therefore responsible for right heart failure as illustrated by our patient; The clinical presentation is variable and depends on age and anatomical form, usually diagnosed on the occasion of cyanosis, right heart failure or cardiac arrhythmia.…”