Case of simultaneous Chiari 1.5 malformation and syringobulbia

Successful treatment of unilateral facial nerve palsy in a pediatric patient with syringobulbia and Chiari malformation type I: illustrative case

“…CN V, VI, VII, IX, X, and XII palsies were all reported. 3,4,6,9 CN IX and X palsies were reported in 15 (27%) of the 55 patients. 3,4,6,9 CN VI palsy was reported in 10 patients (18%), and CN V, VII, and XII were reported in 3 patients.…”

“…3,4,6,9 CN IX and X palsies were reported in 15 (27%) of the 55 patients. 3,4,6,9 CN VI palsy was reported in 10 patients (18%), and CN V, VII, and XII were reported in 3 patients. 3,4,6,9 All CN VII (3, 5%) palsies were bilateral.…”

“…Fifty-one (93%) of 55 cases involved syringobulbia in conjunction with syringomyelia. [2][3][4][5][6][7][8][9][10][11][12][13] Headaches and nystagmus were the most common presenting symptoms of CMI involving syringobulbia, with 33% of patients experiencing these symptoms. [2][3][4][5][6][7][8][9][10][11][12][13] Diplopia (24%), hyperreflexia (24%), ataxia (22%), and dysphagia (22%) were also common symptoms in this cohort.…”

“…[2][3][4][5][6][7][8][9][10][11][12][13] Headaches and nystagmus were the most common presenting symptoms of CMI involving syringobulbia, with 33% of patients experiencing these symptoms. [2][3][4][5][6][7][8][9][10][11][12][13] Diplopia (24%), hyperreflexia (24%), ataxia (22%), and dysphagia (22%) were also common symptoms in this cohort. [2][3][4][5][6][7][8][9][10][11][12][13] Dysarthria (9%), dysesthesia (9%), and dyspnea (4%) were less commonly observed in these patients [2][3][4][5][6][7][8][9][10][11][12][13] (Table 1).…”

“…[2][3][4][5][6][7][8][9][10][11][12][13] Diplopia (24%), hyperreflexia (24%), ataxia (22%), and dysphagia (22%) were also common symptoms in this cohort. [2][3][4][5][6][7][8][9][10][11][12][13] Dysarthria (9%), dysesthesia (9%), and dyspnea (4%) were less commonly observed in these patients [2][3][4][5][6][7][8][9][10][11][12][13] (Table 1).…”