“…The patients were predominantly young (< 40 years) and male [12,23,24,25,26,28,29,30,31,32,33,34,35]. With regard to symptoms leading to diagnosis, in all but two cases the main symptom was abdominal pain (89,5 %) [12,22,23,24,25,26,28,29,30,31,32,33,34,35,36], with few patients presenting with atypical abdominal symptoms (mainly thought to be urolithiasis) [28,30,32]. In the remaining two cases rectal blood loss was the main symptom [10,27].…”