Carpal Tunnel Syndrome Associated with Klippel-Trénaunay-Weber Syndrome

Siegall, Evan; Ratner, Joshua A.

doi:10.2106/jbjs.cc.n.00133

Cited by 2 publications

(2 citation statements)

References 17 publications

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“…Klippel-Trénaunay syndrome is a rare congenital condition characterized by hypertrophy of bone and soft tissue, varicose veins, and cutaneous capillary malformation developing the classical skin port-wine stains [1]. Carpal tunnel syndrome is seldom associated with Klippel-Trénaunay syndrome and only 4 cases (Table 1) have been reported in the medical literature [2][3][4][5]. This is explained by the fact that peripheral neuropathy is rare in Klippel-Trénaunay syndrome.…”

Section: Discussionmentioning

confidence: 99%

“…lippel-Trénaunay syndrome is an uncommon congenital condition that can occasionally affect peripheral nerves [1]. In the medical literature, the median nerve has only been found to be affected in 4 cases [2][3][4][5], but despite this, we believe that sonographic or MRI imaging of the carpal tunnel and the median nerve should be considered pre-operatively.…”

Section: Background and Importancementioning

confidence: 99%

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Carpal Tunnel Syndrome Associated with Klippel-Trénaunay Syndrome: A Case Report

Arenas-Prat¹

2020

Iran J Neurosurg

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Background and Importance: Klippel-Trénaunay syndrome is a rare congenital condition that rarely affects peripheral nerves. Median nerve involvement at the carpal tunnel level has only been reported on four occasions of this syndrome in the medical literature. Case Presentation: A 61-year-old Caucasian female patient with Klippel-Trénaunay syndrome presented with a 10-month history of paraesthesia and numbness affecting the median nerve distribution area of her left hand. The clinical and neurophysiological examination confirmed a moderately severe carpal tunnel syndrome that required surgical decompression. Conclusion: Pre-operative findings demonstrated diffuse vascular infiltration and engorgement of the median nerve. Flexor tendons had a normal appearance. The patient had a satisfactory post-operative period with full resolution of her symptoms 4 weeks after the procedure. Although peripheral nerves are rarely affected in patients with Klippel-Trénaunay syndrome, neurological symptoms could indicate nerve involvement and magnetic resonance imaging (MRI) examination should be considered to further assess the extension of the lesion.

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Section: Discussionmentioning

confidence: 99%

Section: Background and Importancementioning

confidence: 99%