Caroli's disease: an ultrasonic diagnosis

Bass, E. M.; Funston, M. R.; Shaff, Max I.

doi:10.1259/0007-1285-50-593-366

Cited by 23 publications

(3 citation statements)

References 7 publications

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“…Occasionally, mottling of contrast medium over the hepatic surface after cholangiography may indicate the intrahepatic cyst dilatations. 12 The cholangiographic features of Caroli's disease are well established as saccular or fusiform dilatation of the intrahepatic bile ducts. Irregular bile duct walls, strictures, and stones may be present.…”

Section: Discussionmentioning

confidence: 99%

Caroli’s disease: a diagnostic challenge

Yadav¹,

Adhikari²,

Pandit³

et al. 2018

Int Surg J

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Caroli’s disease is a rare congenital hepatobiliary disease characterized by multifocal segmental dilatation of intrahepatic bile ducts affecting all or parts of the liver. It predisposes to biliary stasis and consequent lithiasis, cholangitis, abscesses, and septicemia. Sometimes it is difficult to diagnose and differentiate it from other similar disease conditions. 60-year-old female presented with features of recurrent cholangitis with hepatolithiasis and multiple cyst in liver, cholelithiasis was planned for cholecystectomy and drainage procedure. Patient underwent open cholecystectomy with common bile duct (CBD) exploration with T-tube placement due to intraoperative instability. Post-operative T tube cholangiogram was done. Post-operative T tube cholangiogram showed bilobar major duct cystic dilatation with predominant left lobe involvement, with few cysts containing calculi. Patient was planned for left hepatectomy with bile duct excision but patient refused to undergo aforementioned surgery. Therefore ERCP and sphincterotomy was done in view of poor performance status.Caroli’s disease being a rare disease is sometimes difficult to diagnose and treat in an old age patient with bilobar involvement and poor general conditions.

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Section: Discussionmentioning

confidence: 99%

Caroli’s disease: a diagnostic challenge

Yadav¹,

Adhikari²,

Pandit³

et al. 2018

Int Surg J

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“…Diagnostic confirmation of Caroli's disease is preferentially carried out by ultrasonography (12), by retrograde cholangiography or transhepatic cholangiography, or even by intraoperative cholangiography (11,13). Recently, Starshak et al (14) stated that the diagnosis of Caroli's disease can be accurately and safely established by employing radionuclide hepatocholangiography (RHC), one of the new hepatobiliary imaging agents.…”

Section: Discussionmentioning

confidence: 99%

Caroli's Disease in Childhood

Fagundes‐Neto,

Schettini,

Wehba

et al. 1983

J. pediatr. gastroenterol. nutr.

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SummaryCaroli's disease is a rare congenital disorder characterized by segmentary saccular dilatation of the intrahepatic bile ducts, which manifests itself clinically by cholangitis and bile stones. We report two cases of Caroli's disease in schoolgirls with clinical signs of recurrent abdominal pain associated with intermittent crises of cho‐lestatic jaundice. Diagnosis was made by retrograde cholangiography in one patient and by intravenous cholangiography in the other.

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“…Echotomography [11] and scanning [12] are superior since they clearly demonstrate dilatations and the calculi they contain. Since they have become widely used, we prefer these noninvasive methods to transparietal transhepatic cholangiography or to retrograde cholangiography via retrograde catheterization of the papilla [13].…”

Section: Radiological Studymentioning

confidence: 99%

Caroli's disease

et al. 1984

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In 1958, Caroli [1, 2] was the first to describe congenital dilatations of intrahepatic bile ducts concerning a segment, a sector, a lobe, or both halves of the liver. Sometimes the dilatations are associated with congenital hepatic fibrosis as described in 1954 by Grumbach [3], dilatations of biliary ductules (biliary angiomatosis), and parenchymal sclerosis. This hereditary autosomal recessive disease is associated in many cases with nephrospongiosis or Cacchi‐Ricci's disease [4]. Caroli's disease is quite rare. By 1982, a total of 99 cases had been reported in the world literature. Aside from these cases we have seen and operated on 10 patients [5, 6]. In Caroli's disease, stenosis and dilatations give rise initially to biliary stasis and, secondly, to intrahepatic biliary lithiasis and biliary infection. The normal course in Caroli's disease consists of suppurative cholangitis, septicemia with gram‐negative organisms, and intrahepatic and subphrenic abscesses. The disease must be recognized before these serious complications arise. The new hepatobiliary imaging procedures should now allow an early diagnosis and, therefore, a better therapeutic approach.

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Caroli's disease: an ultrasonic diagnosis

Cited by 23 publications

References 7 publications

Caroli’s disease: a diagnostic challenge

Caroli’s disease: a diagnostic challenge

Caroli's Disease in Childhood

Caroli's disease

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