Cardiogenic Shock in Patient With Acute Installation Pulmonary Hypertension

Abstract

BACKGROUNDAntisynthetase syndrome (ASS) is an autoimmune disease characterized by interstitial lung disease (ILD), inflammatory arthritis and myopathy, skin hyperkeratosis (mechanic's hands) and Raynaud's phenomenon as the main symptoms. The lung is the most involved extramuscular organ in ASS and it defines the course of the disease, with pulmonary arterial hypertension (PAH) being a rare finding and without an established screening. Anti-aminoacyl-tRNA-synthetase (anti-ARS) autoantibodies have been correlated with specific clinical presentations and prognosis.