2019
DOI: 10.1017/s1047951119001562
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Cardiac disease in Kearns-Sayre syndrome requires comprehensive management

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Cited by 2 publications
(3 citation statements)
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“…In addition, bradycardia leading to early afterdepolarizations (EADs) and mitochondrial dysfunction causing delayed afterdepolarizations (DADs) were also suggested as potential causes for the development of VA 11 . Because the presence of fully functioning PPM did not prevent the development of fatal arrhythmias in previous reports of KSS, several authors have suggested implanting ICD for primary prevention instead of PPM only 11,20–22 . However, in our population, none of the KSS patients with a pacemaker in place developed dCA or VA.…”
Section: Discussionmentioning
confidence: 67%
See 1 more Smart Citation
“…In addition, bradycardia leading to early afterdepolarizations (EADs) and mitochondrial dysfunction causing delayed afterdepolarizations (DADs) were also suggested as potential causes for the development of VA 11 . Because the presence of fully functioning PPM did not prevent the development of fatal arrhythmias in previous reports of KSS, several authors have suggested implanting ICD for primary prevention instead of PPM only 11,20–22 . However, in our population, none of the KSS patients with a pacemaker in place developed dCA or VA.…”
Section: Discussionmentioning
confidence: 67%
“…11,[20][21][22] However, in our population, none of the KSS patients with a pacemaker in place developed dCA or VA. In com-…”
mentioning
confidence: 51%
“…These authors suggested that these patients should have regular ECGs to identify conduction system disease which has the potential to develop bradycardia and malignant tachyarrhythmias. Finsterer 17 summarized the comprehensive management needed in patients with Kearns-Sayre syndrome who have cardiac disease. He notes that these patients are at risk for sudden cardiac death and may need pacemaker implantation and eventually implantable cardioverter defibrillators.…”
Section: Discussionmentioning
confidence: 99%