Budd–Chiari syndrome: a focussed and collaborative approach

Mukund, Amar; Sarin, Shiv Kumar

doi:10.1007/s12072-018-9900-z

Cited by 15 publications

(15 citation statements)

References 9 publications

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“…BCS presents with abdominal pain and distension due to ascites, lower limb edema and abdominal wall collaterals. 102 103 It may be acute, subacute or chronic with acute being associated with rapid deterioration. 103 Few patients are asymptomatic and asymptomatic cases usually have large collaterals.…”

Section: Detailed Guidelinesmentioning

confidence: 99%

“… 102 103 It may be acute, subacute or chronic with acute being associated with rapid deterioration. 103 Few patients are asymptomatic and asymptomatic cases usually have large collaterals. BCS should be suspected in patients with acute or chronic liver disease in whom common causes of liver disease have been ruled out.…”

Section: Detailed Guidelinesmentioning

confidence: 99%

“…BCS should be suspected in patients with acute or chronic liver disease in whom common causes of liver disease have been ruled out. 103 …”

Section: Detailed Guidelinesmentioning

confidence: 99%

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Indian College of Radiology and Imaging Evidence-Based Guidelines for Interventions in Portal Hypertension and Its Complications

Mukund

Rana

Mohan

et al. 2021

Indian J Radiol Imaging

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Portal hypertension is a complication of chronic liver disease. Various radiological interventions are being done to aid in the diagnosis of portal hypertension; further, an interventional radiologist can offer various treatments for the complications of portal hypertension. Diagnosis of portal hypertension in its early stage may require hepatic venous pressure gradient measurement. Measurement of gradient also guides in diagnosing the type of portal hypertension, measuring response to treatment and prognostication. This article attempts to provide evidence-based guidelines on the management of portal hypertension and treatment of its complications.

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Section: Detailed Guidelinesmentioning

confidence: 99%

Section: Detailed Guidelinesmentioning

confidence: 99%

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Indian College of Radiology and Imaging Evidence-Based Guidelines for Interventions in Portal Hypertension and Its Complications

Mukund

Rana

Mohan

et al. 2021

Indian J Radiol Imaging

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“…Diseases causing thrombotic hepatic venous outflow obstruction (primary BCS) include: Hypercoagulability disorders (Figure 1 ) (factor V Leiden mutation[ 15 , 16 ], protein C or S and antithrombin-III deficiency), infections/sepsis, oral contraceptive therapy[ 17 - 19 ], pregnancy and post-partum, chronic inflammatory or autoimmune diseases (antiphospholipid syndrome, Behçet, systemic erythematous lupus), mye-loproliferative disorders (polycythemia vera, essential thrombocythemia, myelofibrosis, and paroxysmal nocturnal hemoglobinuria[ 20 , 21 ]), dehydration, chemoradiotherapy, sickle cell disease, paraneoplastic syndromes or neoplastic thrombosis, leiomyosarcoma of the inferior vena cava, complication of liver transplantation[ 22 , 23 ], and total parenteral nutrition[ 24 ].…”

Section: Pathophysiologymentioning

confidence: 99%

Transjugular intrahepatic portosystemic shunt for Budd-Chiari syndrome: A comprehensive review

Inchingolo¹,

Posa²,

Mariappan³

et al. 2020

WJG

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Budd-Chiari syndrome (BCS) is a relatively rare clinical condition with a wide range of symptomatology, caused by the obstruction of the hepatic venous outflow. If left untreated, it has got an high mortality rate. Its management is based on a step-wise approach, depending on the clinical presentation, and includes different treatment from anticoagulation therapy up to Interventional Radiology techniques, such as transjugular intrahepatic portosystemic shunt (TIPS). TIPS is today considered a safe and highly effective treatment and should be recommended for BCS patients, including those awaiting orthotopic liver transplantation. In this review the pathophysiology, diagnosis and treatment options of BCS are presented, with a special focus on published data regarding the techniques and outcomes of TIPS for the treatment of BCS. Moreover, unresolved issues and future research will be discussed.

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“…Budd-Chiari syndrome (BCS) was described by George Budd and Hans Chiari [1], which is associated with hepatic venous outflow tract obstruction by thrombosis or structural compression at the level of the main hepatic vein (HV) or the extrahepatic segment of the inferior vena cava (IVC) [2]. The clinical manifestation of BCS may be asymptomatic until cause acute liver failure.…”

Section: Introductionmentioning

confidence: 99%

First Report of Fulminant Budd-Chiari Syndrome Treated by Direct Intrahepatic Portocaval Shunt in Vietnam

Nguyen

Dong

et al. 2021

Case Rep Gastroenterol

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Budd-Chiari syndrome (BCS) is a rare disorder caused by hepatic venous outflow obstruction that can lead to acute liver failure proposing liver transplantation or transjugular intrahepatic portosystemic shunt. However, the transjugular intrahepatic portosystemic shunt is not always successful due to the entire hepatic vein thrombosis while transplantation is not unfailingly feasible. In these situations, the direct intrahepatic portosystemic shunt (DIPS) is a viable alternative that may ameliorate portal hypertension in these patients. We described a case of a 21-year-old male with fulminant hepatic failure owning to BCS with a 4-day history of abdominal pain and nausea. Laboratory workup, including viral, autoimmune etiologies JAK2 mutation, Factor V Leiden, antiphospholipid antibody syndrome, was negative. The patient’s clinical status worsened with hepatic encephalopathy stage II despite administering anticoagulation. Thus, the patient underwent urgently DIPS after unaccessible to the creation of a transjugular intrahepatic portosystemic shunt and impossible to transplantation. The patient’s health was improved and discharged. Fulminant Budd-Chiari is a rare disease to be demanding prompt treatment. While transplantation or transjugular intrahepatic portosystemic shunt is failed, the DIPS is considered an alternative candidate associated with clinical improvement.

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Budd–Chiari syndrome: a focussed and collaborative approach

Abstract: Hepatology International (2018) 12:483-486 https://doi.org/10.1007/s12072-018-9900-z( 0123456789().,-volV) (0123456789(). ,-volV)

Cited by 15 publications

References 9 publications

Indian College of Radiology and Imaging Evidence-Based Guidelines for Interventions in Portal Hypertension and Its Complications

Indian College of Radiology and Imaging Evidence-Based Guidelines for Interventions in Portal Hypertension and Its Complications

Transjugular intrahepatic portosystemic shunt for Budd-Chiari syndrome: A comprehensive review

First Report of Fulminant Budd-Chiari Syndrome Treated by Direct Intrahepatic Portocaval Shunt in Vietnam

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