Budd-Chiari Syndrome

A Unique Case of the Transformation of a Hepatic Leiomyoma into Leiomyosarcoma with Pancreatic Metastases: Review of the Literature with Case Presentation

“…The first author to describe a case of primary leiomyoma of the liver was Demel [3] in 1926, presenting the case of a patient with a 12 cm lesion to the right lobe of the liver. Conversely, the first official report of primitive leiomyosarcoma of the liver occurred in 1926 by Beaird [4] who described a lesion likely departing from the muscular wall of the portal vein. From that moment, there have been different descriptions with cases rather simple to diagnose, frankly benign, and cases that appeared immediately malignant.…”

“…Author Localization, Measure (cm) Symptoms Histological Diagnosis Demel [3] RL/12 RUQ pain Leiomyoma BEAIRD JB [4] Portal vein RUQ pain Leiomyosarcoma Dalenz [5] LL/NS RUQ pain Leiomyoma Masur [6] RL/NS NS Leiomyosarcoma (2) Bloustein [7] RL/3.3 RUQ pain Leiomyosarcoma Maki [8] RL/NS NS Leiomyosarcoma Griffin [9] Cava vein NS Leiomyosarcoma Shurbaji [10] RL/NS RUQ pain Leiomyosarcoma Kinoshita [11] RL/NS RUQ pain Leiomyosarcoma Rummeny [12] NS NS Leiomyoma Herzberg AJ [13] RL/19 RUQ pain Leiomyoma Little [14] LL/NS NS Leiomyoma Lee [15] Hepatic vein RUQ pain Atypical Leiomyoma Spagliardi [16] RL/NS None Leiomyosarcoma Sundaresan [17] Portal vein RUQ pain Leiomyosarcoma Bartoli [18] RL/NS NS Leiomyoma Ishii [19] 34 cases / Leiomyosarcoma Korbi [20] RL/2.1 None Leiomyosarcoma Reinertson [21] LL/10 RUQ pain Leiomyoma Ross J S [22] RL/3.3 RUQ pain Leiomyosarcoma (HIV) Baur [23] RL/NS RUQ pain Leiomyosarcoma Saint-Paul [24] RL/9.3 RUQ pain Leiomyosarcoma Prévot S [25] RL/NS RUQ pain Leiomyoma in HIV Hiyama [26] RL/NS None Leiomyosarcoma Abdelli [27] RL/NS RUQ pain and fever Leiomyosarcoma Davidoff [28] RL/NS RUQ pain Leiomyoma in transplantation Yoon [29] RL/NS RUQ pain Myxoid Leiomyoma Yanase [30] RL/12 RUQ pain Leiomyoma with Cystoadenoma Enoki [31] Hepatic vein RUQ pain Leiomyosarcoma Mesenas [32] RL/3.6 None Leiomyoma Tsuji [33] RL/NS RUQ pain Leiomyosarcoma Belli [34] RL and LL/30 Obstruction Giant leiomyoma Torres [35] RL/NS RUQ pain Leiomyosarcoma Fujiita [36] RL/NS RUQ pain Leiomyosarcoma Lee [37] RL/NS RUQ pain Leio...…”

Right Atrial Maass Associated with Hepatoma -2 Case Reports-

“…There are several reports about secondary cardiac malignancy. Hepatoma, testicular teratoma and smooth muscle sarcoma may cause the right atrial tumor growth through the inferior vena cava 1 , 5 – 7 ) . Especially, hepatocellular carcinoma is known for its tendency to grow in the venous system.…”

Budd-Chiari-Syndrom bei retroperitonealem Neurinom

“…Das Auftreten des Budd-Chiari-Syndroms gibt dann lediglich über die Ausbreitung des neoplastischen Prozesses Aufschluß. Bei rechtzeitiger Diagnosestellung soll allerdings die Prognose der primären Sarkorne der Vena cava günstiger sein, da diese Tumoren erst spät metastasieren (4,14,35). Bisher wurden zehn Fälle von Leiomyosarkorn der unteren Hohlvene mit Budd-Chiari-Syndrom mitgeteilt (14,17,33).…”