Bowel‐associated dermatosis‐arthritis syndrome, a diagnostic challenge in a young child with very early‐onset inflammatory bowel disease

Abstract

A 14‐month‐old girl with very early‐onset inflammatory bowel disease (VEO‐IBD) was admitted with a flare of her bowel disease and subsequently developed high fevers, joint pain, and skin lesions during her hospitalization. Workup demonstrated bowel‐associated dermatosis‐arthritis syndrome in the setting of VEO‐IBD, a neutrophilic dermatosis rarely reported in children that can be challenging to diagnose and treat, with limited literature for patients under 2 years of age.