Bladder Cancer in a Long-term Survivor of the Prune Belly Syndrome

Kondo, Fuki; Matsumoto, Fumi; Suenaga, Shinta; Matsui, Futoshi; Yazawa, Koji; Nagahara, Akira; Nishimura, Kazuo; Ishizuya, Yu

doi:10.1016/j.urology.2021.11.028

Cited by 1 publication

(2 citation statements)

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“…PBS is associated with urogenital and extra-urogenital anomalies. The extra urogenital anomalies include cardiopulmonary, gastrointestinal and musculoskeletal and orthopaedic anomalies [1] [18] [23] [24] [25]. In this study, 2 patients had patent urachus as shown in Figure 8 and Figure 9.…”

Section: Discussionmentioning

confidence: 81%

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Prune Belly Syndrome: A Ten-Year Single Tertiary Centre Experience in South-South, Nigeria

Abhulimen¹,

Francis²

2023

OJU

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Background: Prune belly syndrome (PBS) is a congenital anomaly that consists of a triad of abdominal wall defect, bilateral cryptorchidism, and urinary tract dilation. The disease is of varying severity. This study aims to highlight the challenges and peculiarities in the management of PBS in a resource-poor setting. Materials and Methods: This is a ten-year retrospective study conducted at the University of Port Harcourt Teaching Hospital. Ethical approval for the study was sought and gotten from the hospital's ethical committee. The information gotten included history, duration of symptoms, examination findings, age of the patient, category of disease, and intraoperative findings. The data from the folders were collected and evaluated. Frequencies, percentages, the mean and standard deviation were used to summarize the data as appropriate. Results: Fifteen patients were included in the study. The hospital incidence of PBS was 112/100,000, twelve males and three females. The age range was from 1 day to 15 years, mean age was 14 months ± 2.3 months. Most patients presented between 3 months and 2 years and 11 months. Twelve patients had category three PBS and five patients had associated anomalies. Eleven male patients died after 5 years of follow-up from progressive renal deterioration. The female patient fared better than the males. Conclusion: PBS is rare, most patients with the condition present late. The most common cause of mortality was progressive renal deterioration.

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Section: Discussionmentioning

confidence: 81%

“…Follow-up is also important for these patients; the patients should have serial renal function tests. There are reports of developing renal failure and bladder malignancy later in life [25].…”

Section: Discussionmentioning

confidence: 99%

Prune Belly Syndrome: A Ten-Year Single Tertiary Centre Experience in South-South, Nigeria

Abhulimen¹,

Francis²

2023

OJU

View full text Add to dashboard Cite

show abstract

Bladder Cancer in a Long-term Survivor of the Prune Belly Syndrome

Cited by 1 publication

References 13 publications

Prune Belly Syndrome: A Ten-Year Single Tertiary Centre Experience in South-South, Nigeria

Prune Belly Syndrome: A Ten-Year Single Tertiary Centre Experience in South-South, Nigeria

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