Bi̇r Yeni̇doğanda Epi̇gnatus – Orofari̇ngeal Teratom

Abstract

Epignathus also known as oropharyngeal teratoma is a very rare tumor in newborns, which has a female predominance. The treatment is simple excision of the mass surgically which should not be delayed. We operated a male newborn due to intraoral mass causing episodic deglution and respiration problems. The histopathology was reported as epignathus and this case is discussed based on the current literature because of its rarity.

Sequelae of congenital oropharyngeal teratoma in the oral cavity of the child

“…Although congenital oropharyngeal teratomas are considered rare benign tumors, when present, they can cause several sequelae in the child's oral cavity, as observed in this case report, requiring long-term multidisciplinary follow-up to correct them. This clinical case has many similarities with others found in the literature 2,[6][7][8]10,11,[15][16][17][18][19] . Regarding gender, most studies reported the presence of oropharyngeal teratomas in female children.…”

“…In this case, the removal of the teratoma was performed early, o the 17th day of life, requiring removal of the residual teratoma two weeks later. The tumor described in this case was classified anatomically and pathologically as mature, as well as the tumors reported by most authors 2,4,6,9,11,12,14,16,19,21,22 . However, even though it is an uncommon occurrence, Kumar et al 7 and Chung et al 8 reported cases of immature teratoma.…”

“…The presence of the larger tumor was found during the ultrasound exam in the 34th week of pregnancy, similar to other reports 9,10,12,16,19 in which the diagnosis also occurred in the third trimester. Other studies 7,8,20,23 reported the presence of teratoma in the second trimester of pregnancy, and in some 2,14,15 , only after birth. According to Tonni et al 1 and Kumar et al 10 , the presence of teratoma can be identified early in the 15th to 16th week of gestation, thus allowing delivery and postpartum maneuvers to be planned, increasing the child's survival.…”

“…Studies show a higher prevalence, in the proportion of 3:1, in girls than in boys, without justification for the difference between them. Other studies 3,[12][13][14]21,22 described the presence of teratoma in male neonates. In this case, it was not possible to define the etiology of congenital oropharyngeal teratoma.…”

“…Most studies 2,4,[6][7][8][9][10][11][12][13][14][15] report some characteristics of teratoma and its removal, without describing the consequences in the oral cavity. Whereas congenital oropharyngeal teratoma develops early in intrauterine life, thus affecting the growth and development of adjacent structures, the purpose of this case report is to present the sequelae of this tumor in a child's oral cavity.…”