Biochemical and Physiological Characterization of the Urinary Bladder in Ehlers-Danlos Syndrome

Deveaud, Catherine M.; Kennedy, William A.; Zderic, Stephen A.; Howard, Pamela S.

doi:10.1007/978-1-4615-4737-2_16

Cited by 4 publications

(1 citation statement)

References 18 publications

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“…Table summarizes the design and publication date characteristics of the 105 included studies . Studies consisted of case reports/series (N = 62, 60%) and observational studies (N = 43, 40%), including cross sectional (N = 29), case‐controlled (N = 12), and cohort (N = 2) designs.…”

Section: Resultsmentioning

confidence: 99%

Urogenital and pelvic complications in the Ehlers‐Danlos syndromes and associated hypermobility spectrum disorders: A scoping review

2019

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The Ehlers-Danlos syndromes (EDS) and associated hypermobility spectrum disorders (HSD) are a heterogenous group of connective tissue disorders associated with significant morbidity. The urogenital aspects of these disorders are understudied and there is little guidance on the prevalence, types, or outcomes of urogenital complications in EDS/HSD. Our objective was to perform a scoping review to characterize and synthesize the literature reporting urogenital and pelvic complications in EDS/HSD patients. We performed a systematic search of three databases (Medline, CINAHL, Embase) to January 2019. English language, full-text articles reporting on urogenital or pelvic complications in EDS/HSD were included. A total of 105 studies were included (62 case reports/series, 43 observational) involving patients with hypermobile (23%), vascular (20%), classical (12%) EDS, and HSD (24%). Some studies looked at multiple subtypes (11%) or did not report subtype (33%). Reported complications included urinary (41%), gynecological (36%), obstetrical (25%), renal (9%), and men's health problems (7%), with some studies reporting on multiple areas. Urinary and gynecological complications were most prevalent in patients with HSD, while a broad range of complications were reported in EDS. While further research is required, results suggest a higher index of suspicion for urogenital problems is probably warranted in this population.

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Section: Resultsmentioning

confidence: 99%

Urogenital and pelvic complications in the Ehlers‐Danlos syndromes and associated hypermobility spectrum disorders: A scoping review

2019

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Neuromuscular Dysfunction of the Lower Urinary Tract

Wein¹,

Dmochowski²

2012

Campbell-Walsh Urology

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Complexities of management of a urostomy in Ehlers-Danlos syndrome: a reflective account

Oxenham

2016

Br J Nurs

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Mary (pseudonym) is a 30-year-old woman who underwent a urinary diversion and formation of an ileal conduit/urostomy (urinary stoma) due to the formation of multiple bladder diverticula, which caused micturition difficulties and recurrent urinary tract infections with associated pain and discomfort. The bladder diverticula were caused by Ehlers-Danlos syndrome (EDS), a hereditary disorder of the connective tissue or, particulary, defective collagen. Surgical intervention in patients with EDS is prone to complications due to poor wound healing, including issues of dehiscence, postoperative bleeding and poor uptake of anaesthesia and analgesia. After an initial presentation of the syndrome of EDS and Mary's history, this article offers a reflective account (informed by Gibbs' Reflective Cycle) and illustrates the complexities of caring for an individual with EDS who undergoes stoma formation. The author, a stoma care nurse, demonstrates how using purposeful reflection resulted in better understanding and awareness of caring for an individual with a rare syndrome and the nursing challenges this presented.

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Biochemical and Physiological Characterization of the Urinary Bladder in Ehlers-Danlos Syndrome

Cited by 4 publications

References 18 publications

Urogenital and pelvic complications in the Ehlers‐Danlos syndromes and associated hypermobility spectrum disorders: A scoping review

Urogenital and pelvic complications in the Ehlers‐Danlos syndromes and associated hypermobility spectrum disorders: A scoping review

Neuromuscular Dysfunction of the Lower Urinary Tract

Complexities of management of a urostomy in Ehlers-Danlos syndrome: a reflective account

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