Bilateral Pheochromocytoma with Hypertrophic Obstructive Cardiomyopathy: A Rare Case

Abstract

Pheochromocytomas are catecholamine-secreting tumors of neuroectodermal origin. Different clinical presentations, various preoperative and intraoperative complications and their potential to become malignant provide a challenge in diagnosing and managing these cases. We report a rare case of bilateral pheochromocytoma with hypertrophic obstructive cardiomyopathy. He was diagnosed with bilateral pheochromocytoma with hypertrophic obstructive cardiomyopathy presenting at the age of 15 years without evidence of multiple endocrine neoplasia type 2 (MEN-2), or any familial syndrome or metastasis and then offered a surgery which was first cancelled due to uncon trolled hypertension. He was then taking alpha blocker for 8 years until he was again admitted to our institute. After prior blood pressure control with alpha and beta blocker drugs, open bilateral adrenalectomy was done without any complications. intraoperative spikes in blood pressure was managed with short acting antihypertensives, such as esmolol and labetalol. Postoperatively, patient is given steroid and under follow-up to rule out malignancy and other complications.