“…Several fatalities directly attributable to the systemic involvement by the disease have been reported [16][17][18][19][20], and the risk of progression to SLE is well known [13]. Furthermore, many studies have shown that a wide spectrum of immune diseases ranging from arthritis and adult Still's disease [14,21] to polymyositis [22], interstitial lung disease [23], scleroderma [24], vasculitis [8], uveitis [25], thyroiditis [26], or drug hypersensitivity [27,28] may be associated with Kikuchi Fujimoto disease at presentation or may complicate the ensuing course. Other investigators have also described the association with neurologic disorders [29,30], infection with HIV [31] and HTLV-1 [32], hemophagocytic syndrome [11,12], and breast cancer [33] or lymphoma [34].…”