Bilateral congenital dislocation of the patella associated with synostosis of proximal tibiofibular and proximal radioulnar joints: A case report

Gökhan, İlyas; Eren, Toygun Kağan; Kaptan, Ahmet Yiğit; Ulucaköy, Coşkun; Kanatlı, Ulunay

doi:10.5606/ehc.2018.61318

Cited by 3 publications

(3 citation statements)

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“…Most patients in previous review had a flexion knee contracture with difficult walking. It is reported that when the ability to extend the knee is preserved, CDP does not lead to functional failure and it is likely that the pathology comes at the attention of the physician during the adulthood [ 3 , 11 , 16 , 17 , 18 ].…”

Section: Discussionmentioning

confidence: 99%

“…İlyas reported the case of bilateral CDP with synostosis of proximal tibiofibula, proximal radioulnar joint in a 30-year-old man which underwent extensive lateral retinacular release when he was 13 years old. The patient complained of pain and recurrent dislocation of the left patella but he did not accept a further surgical treatment as his pain was not affecting his daily life [ 17 ].…”

Section: Discussionmentioning

confidence: 99%

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Congenital Dislocation of the Patella – Surgical Treatment Rationale and Literature Review

Pedrotti

Bertani

Rosa

et al. 2021

JOCR

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Introduction: Congenital dislocation of the patella (CDP) is a rare condition and its treatment is not well defined. In CDP, patella is dislocated on the lateral aspect of the distal femur, laterally from the trochlear groove, it cannot be reduced manually and it is almost always associated with genu valgum, lateral torsion of the proximal tibia, and flexion contracture of the knee. This condition is present at birth, but the clinical findings can be subtle at birth due to the size and character of the structures being examined; early diagnosis is essential, but it may be delayed to late childhood or adulthood. If CDP is not promptly treated, the disability increases during growth, so surgical correction should be planned as soon as the diagnosis is confirmed. Case Report: We report a case of bilateral CDP associated with bilateral proximal radioulnar joint stiffness; the patient at the age of diagnosis was 11 years old and underwent a bilateral delayed surgical procedure; the 4-year follow-up results are satisfactory. Surgical treatment rationale and literature are reviewed. Conclusion: Surgical correction for CDP is generally recommended, but there is no agreement in literature on the ideal treatment and in some cases, with mild impairment of the knee function, observation alone has been suggested. The decision about a surgical treatment can be difficult and depends on the degree of disability of the patient. Keywords: Congenital dislocation of the patella, bilateral congenital dislocation, patella, Z-plasty quadriceps muscle, lateral retinaculum release, lack of active knee extension.

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Section: Discussionmentioning

confidence: 99%

Section: Discussionmentioning

confidence: 99%

Congenital Dislocation of the Patella – Surgical Treatment Rationale and Literature Review

Pedrotti

Bertani

Rosa

et al. 2021

JOCR

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“…toz gibi genetik hastalıkları ve özellikle uzun kemiklere yerleşme eğilimi olabilen birçok benign ve malign tümörleri içerir (13)(14)(15).…”

Section: Sonuçunclassified

17 Yaşında Erkek Hastada Sol Proksimal Tibiada Ağrısız Lezyon: Adamantinoma

Erboğa¹,

Engin²,

Pervane³

et al. 2020

Akd Med J

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ÖZAdamantinomalar nadir görülen low grade malign kemik tümörleridir. En sık 20-30 yaşlar arasında görülürler ve erkeklerde daha sık görülme eğilimindedirler. En sık yerleşim yeri tibiadır. Hastalar en sık ağrılı ya da ağrısız bir şişlik ile başvururlar. Radyografisi agresiftir. Tedavisi tümörün geniş rezeksiyonu ve rekonstrüksiyondur. Kemoterapi faydasızdır ve radioresistanttır. Uzun dönem sağkalımı iyidir. Bu çalışmada 17 yaşında erkek hastada tibia proksimal yerleşimli adamantinoma olgusunu sunduk. Başarılı tedavisi yapılan hasta halen takibimiz altındadır. ABSTRACTAdamantinomas are rare low grade malignant bone tumors. They are most common between the ages of 20 and 30 and are slightly more common in men. The most common localization is the tibia. The patients present with a painful or painless swelling and the lesion seems to be aggressive on radiography. The treatment is extensive resection of the tumor and reconstruction. Chemotherapy is useless as the lesions are radioresistant. The long term prognosis is good. In this study, we present a case of adamantinoma located at the proximal section of the tibia in a 17-year-old male patient. The treatment was successful and the patient is still under follow-up. GIRIŞAdamantinoma, mikroskobik olarak hafif bir iğ hücresiyle çevrili epitelial hücre kümeleriyle karakterize edilen düşük dereceli bir malign neoplazmdır (1). Tüm primer kemik tümörlerinin %1'inden azını oluşturan nadir bir tümördür (2).En sık görüldüğü yaş aralığı 20-50 yaş arasıdır ve erkeklerde daha sık görülür. Tibia, en çok etkilenen bölgedir (raporların %85'i) (3-6).En sık klinik bulgular sırasıyla ağrı ve lokalize şişliktir (7). Radyografisinde genellikle agresif bir pattern sergiler, yer yer radyolüsen alanlar içeren kötü sınırlı sklerotik bir lezyon görülür (8). Adamantinoma tedavisi lezyonun geniş rezeksiyonu ve kemik defektinin rekonstrüksiyonudur (9,10).Kemoterapi veya radyoterapinin tedavide yeri yoktur. Lokal rekürrens ve uzak metastaz nadirdir, metastaz gelişirse en sık akciğerlere gelişir (7,9,10).Biz bu çalışmada sağ tibia proksimali yerleşimli adamantinoması olan bir hastanın presentasyon, görüntüleme bulguları, tedavisi ve takibini tanımladık.

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