Bilateral cochlear implantation in bilateral Langerhans cell histiocytosis

Abstract

Surgical excision of LCH lesion remains a mainstay of treatment for temporal bone involvement. Bilateral cochlear implant with adjuvant immunosuppression in our patient demonstrated both immediate and delayed improvement in auditory function after staged cochlear implantation in the setting of persistent disease.

Case report: Langerhans cell histiocytosis of the temporal bone in children: Challenging diagnosis of a rare disease with some pitfalls

“… 32 , 33 However, there are reports of successful cochlear implantation to restore hearing ability. 34 , 35 , 36 Even if there is no initial hearing loss, several authors report progressive bilateral hearing loss following treatment. Nandurie et al observed hearing loss in 38% of their patients 5 years post‐therapeutically.…”

“… 32 , 33 However, there are reports of successful cochlear implantation to restore hearing ability. 34 , 35 , 36 …”

“…After treatment, there may be bone re‐mineralization and re‐constitution of the labyrinth, 30 but the sensineuronal hearing loss usually persists, 7,28,31 except for extremely rare cases 32,33 . However, there are reports of successful cochlear implantation to restore hearing ability 34–36 Even if there is no initial hearing loss, several authors report progressive bilateral hearing loss following treatment.…”