Bilateral absence of the superior vena cava. Case report and literature review

Derbel, Bilel; Krarti, N.; Ghédira, Faker; Mrad, M. Ben; Hedhli, M.; Ziadi, J.; Denguir, Raouf

doi:10.1016/j.jdmv.2019.06.005

Cited by 4 publications

(6 citation statements)

References 13 publications

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“…Errors in bridging and regressions lead therefore to the myriad of known caval anomalies. Non‐regression of both common anterior cardinal veins leads to a bilateral SVC, whereas regression of the right common anterior cardinal vein and non‐regression of the left common anterior cardinal vein leads to a persistent left SVC 8 …”

Section: Discussionmentioning

confidence: 99%

“…Non-regression of both common anterior cardinal veins leads to a bilateral SVC, whereas regression of the right common anterior cardinal vein and non-regression of the left common anterior cardinal vein leads to a persistent left SVC. 8 In the case of a bilateral absence of both SVC, this is most likely due to regression of both common anterior cardinal veins. As an adaptive measure, likely analogous to SVC syndrome, 9 other venous systems tend to dilate and, due to the lack of a rigid wall, become varicose, allowing them to cope with and thus drain the blood from the upper extremities and head, ranging from just the more central azygos system to the more distal pelvic and subcutaneous veins, such as was seen in our case (Figure 2).…”

Section: Discussionmentioning

confidence: 99%

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Incidental finding of a bilateral absence of the superior vena cava

Al‐Sewaidi

Smaczny

Ranft

2023

Clinical Case Reports

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Section: Discussionmentioning

confidence: 99%

Section: Discussionmentioning

confidence: 99%

Incidental finding of a bilateral absence of the superior vena cava

Al‐Sewaidi

Smaczny

Ranft

2023

Clinical Case Reports

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“…Patients with this condition are usually asymptomatic, but it is often associated with other cardiac anomalies. 4 Moreover, most congenital heart diseases are also known to be associated with conduction abnormalities. 5 One report suggested that rhythm abnormalities associated with congenital absence of the right SVC have been reported to be as high as 36% and occurs in 70% of patients with congenital absence of the right SVC over 60 years old.…”

Section: Discussionmentioning

confidence: 99%

Successful implantation of a leadless pacemaker in a patient with complete atrioventricular block and congenital absence of superior vena cava: a case report

Kawaguchi

Yatsu

Shiozawa

et al. 2021

European Heart Journal - Case Reports

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Background Congenital absence of superior vena cava (CASVC) is an extremely rare vascular anomaly often associated with conduction disturbances which makes implantation of a pacemaker difficult. We report a case of pacemaker implantation in a patient presenting with complete atrioventricular block (c-AVB) with bilateral absence of the SVC. Case summary A 68-year-old man who had experienced dyspnoea on exertion by c-AVB was admitted to our hospital for treatment and management. Permanent pacemaker insertion was initially planned; however, an endocardial pacemaker lead could not be implanted in the right atrium. Computed tomography scan with contrast revealed that the venous blood from the upper half of the body flowed into the inferior vena cava via the azygos vein. Due to the difficulty of inserting an endocardial lead from the subclavian vein, a leadless pacemaker (LP) was implanted instead via the femoral vein. Discussion This is the first case of an LP implantation in a patient presenting with c-AVB with CASVC. Confirmation of blood vessel anatomy to rule out CASVC is necessary prior to pacemaker implantation when abnormal venous anatomy is suspected.

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“…Long-term cardiac and abdominal ultrasound examination follow-up may be essential as these patients may be predisposed to portal hypertension due to higher pressure in the IVC due to increased blood volume. 8…”

Section: Commentmentioning

confidence: 99%

Absent Superior Vena Cava: An Uncommon Cause of Anomalous Systemic Venous Return

Kaskar,

Sheth,

Paanwala

et al. 2023

World J Pediatr Congenit Heart Surg

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We report a case of a one-year-old boy with tetralogy of Fallot, who was preoperatively diagnosed to have an associated systemic venous anomaly. Computed tomography confirmed the absent superior vena cava, and the case was managed with an appropriate cannulation strategy. Preoperative diagnosis and thorough planning of this rather benign anomaly were imperative for the successful outcome of this case. Clinical and surgical implications of this anomaly are discussed in this report.

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Bilateral absence of the superior vena cava. Case report and literature review

Cited by 4 publications

References 13 publications

Incidental finding of a bilateral absence of the superior vena cava

Incidental finding of a bilateral absence of the superior vena cava

Successful implantation of a leadless pacemaker in a patient with complete atrioventricular block and congenital absence of superior vena cava: a case report

Absent Superior Vena Cava: An Uncommon Cause of Anomalous Systemic Venous Return

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