�ber die vascul�re Neurofibromatose, nach Untersuchungen am menschlichen Magen-Darmschlauch

Haemangiopericytoma of the small intestine, a report of three cases

“…Helwig and Rainier (1953) collected 10 cases of polypoid tumours in the stomach, and listed the various names under which similar tumours have been described in the literature. These include 'fibroma' (Konjetzny, 1920), 'granuloma with eosinophilic infiltration' (Vanek, 1949); 'neurofibroma' (Feyrter, 1949) T h e 3 cases occurring i n the jejunum which we have presented resembled the fibroid polyp of the stomach both macroscopically and microscopically, and we agree with Helwig and Rainier (1953) that the nature of these tumours is inflammatory rather than neoplastic. T h e term ' haemangiopericytoma' has, perhaps, been used to include a number of different conditions.…”

Ruptured Popliteal Aneurysm Resulting from Neurofibromatosis

“…The nodular form affects small arteries and is characterized by a nodular growth of spindle or epithelioid cells between the media and the adventitia. The advance intimal form, added by Feyrter 12 in 1949, shows intimal fibrous thickening and spindle cells throughout the arterial wall. He introduced the term vascular neurofibromatosis.…”

“Vascular Neurofibromatosis” and infantile Gangrene

“…The vascular changes may be slowly progressive [Schurch et al, 19753 and should be diagnosed as early as possible. Identical vascular changes have been reported in patients without CAL spots and neurofibromas [Feyrter, 1949;Brunner et al, 1974;Khalatbary, 19591. These patients do not meet the current diagnostic criteria of NF I or NF 11, yet they have been diagnosed as having vascular NF and have created considerable diagnostic difficulties (as patient l in this study).…”

“…Neither parent had NFvR. DISCUSSION Vascular changes are common in autopsies of NFvR patients [Reubi, 1945;Feyrter, 1949;Fienman and Yakovac, 1970;Salyer and Salyer, 19741. Prior to death, they appear to be mostly subclinical.…”