Athetoid Movements as Initial Manifestation of Primary Sjögren
                        Syndrome

Alvarado-Franco, Norma L.; Marqués, Catalina González; Olguín-Ramírez, Leticia A.; Garza-Alpirez, Alejandro; Femat-Roldán, Giovana; Martínez-Ramírez, Daniel

doi:10.5334/tohm.419

Cited by 3 publications

(2 citation statements)

References 6 publications

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“…CNS involvement generally precedes the diagnosis of primary SS and occurs as recurrent, episodic, which is separated by long disease-free intervals resulting in insidious and progressive neurologic deficits 3 . The incidence of SS patients developing movement disorder is about 2% 13 . Our patient presented with chorea without a family history, and no other etiology of the chorea could be determined.…”

Section: Clinical Discussionmentioning

confidence: 99%

MRI of the brain mimicking autoimmune encephalitis in Sjögren syndrome with chorea: a case report

Gajurel

Giri

Poudel

et al. 2023

Annals of Medicine &Amp; Surgery

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Introduction and importance: Neurologic manifestations in primary Sjögren syndrome (SS) range in prevalence from 8 to 49%, and most of the studies suggest a prevalence of 20%. The incidence of SS patients developing movement disorders is about 2%. Case presentation: The authors herein report a case of a 40-year-old lady with MRI of the brain mimicking autoimmune encephalitis in SS who presented with chorea. Her MRI findings revealed T2 and FLAIR (fluid-attenuated inversion recovery) high signal intensity areas in bilateral middle cerebellar peduncles, dorsal pons, dorsal midbrain, hypothalami, and medial temporal lobes. Clinical discussion: There is still no evidence to support the definite use of MRI in characterizing the central nervous system involvement in primary SS, especially due to overlapping findings with age and cerebrovascular disease. Multiple areas of increased signal intensity in periventricular and subcortical white matter in FLAIR and T2-weighted image is commonly seen in primary SS patients. Conclusion: It is crucial to consider autoimmune diseases like SS as a cause of chorea in adults, even in those whose imaging findings are suggestive of autoimmune encephalitis.

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Section: Clinical Discussionmentioning

confidence: 99%

MRI of the brain mimicking autoimmune encephalitis in Sjögren syndrome with chorea: a case report

Gajurel

Giri

Poudel

et al. 2023

Annals of Medicine &Amp; Surgery

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“…Three patients were diagnosed with lupus-related and vasculitis-related chorea. Chorea may be a classic, albeit rare, manifestation of lupus [8,10,22], but it can also occur as part of other immunologic syndromes including Sjogren´s syndrome and rheumatoid arthritis [8,10,[23][24][25][26].…”

Section: Discussionmentioning

confidence: 99%

The enduring enigma of sporadic chorea: A single center case series

Garcia Ruiz,

Feliz,

Feliz

et al. 2023

Tremor and Other Hyperkinetic Movements

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Chorea can have a wide variety of causes including neurodegenerative, pharmacological, structural, metabolic, infectious, immunologic and paraneoplastic processes.We reviewed the clinical records of patients with apparently sporadic choreic movements and no relevant family history, who presented to our neurology department (Hospital Fundación Jimenez Diaz) between 1991 and 2022.We detected 38 cases of apparent sporadic chorea (ASC); Our analysis revealed 5 cases of genetic chorea (including 3 cases with Huntington´s disease) while 6 cases were autoimmune/hematological; 6 drug-related chorea, 5 metabolic-vascular, 5 due to miscellaneous conditions and 4 were of mixed etiology. No clear etiology was identified in 8 cases. The differential diagnosis of ASC is extensive and challenging. Highlights• Chorea can have a wide variety of genetic and sporadic causes• We reviewed the clinical records of patients with apparently sporadic chorea (ASC), who presented to our neurology department over the last 30 years • We detected 38 cases of apparent ASC; Our analysis revealed a wide array of different sporadic conditions and 5 cases of genetic chorea • The differential diagnosis of ASC is extensive and challenging Garcia Ruiz et al. Tremor and Other Hyperkinetic Movements

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Primary Sjögren’s Syndrome Presenting with Dyskinesia

Chung,

Lee,

et al. 2024

J Korean Neurol Assoc

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Sjögren’s syndrome (SS) is an autoimmune disease in which lymphocytes invade salivary and tear glands, leading to dry mouth and dry eyes. It is also associated with extraglandular manifestations. The most frequently reported neurological extraglandular manifestations are sensory polyneuropathies. Movement disorders have been reported in only 2% of primary SS patients. In this case, we present a case of primary SS initially manifesting as generalized chorea, which was initially misdiagnosed as tardive dyskinesia.

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Athetoid Movements as Initial Manifestation of Primary Sjögren Syndrome

Cited by 3 publications

References 6 publications

MRI of the brain mimicking autoimmune encephalitis in Sjögren syndrome with chorea: a case report

MRI of the brain mimicking autoimmune encephalitis in Sjögren syndrome with chorea: a case report

The enduring enigma of sporadic chorea: A single center case series

Primary Sjögren’s Syndrome Presenting with Dyskinesia

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