Association of Sweet's Syndrome and Systemic Lupus Erythematosus

Barton, Jennifer L.; Pincus, Laura; Yazdany, Jinoos; McCalmont, Timothy H.; Gensler, Lianne S.; Dall’Era, Maria; Fye, Kenneth H.

doi:10.1155/2011/242681

Cited by 7 publications

(9 citation statements)

References 22 publications

(17 reference statements)

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“…The same observation was also made in the cases reported by Batron et al. (two out of three) and Kassardjian et al. (one case) in which the diagnosis of SS was established without fulfilling two minor criteria (no fever at presentation, no underlying cause detected, and three out of four laboratory features not present).…”

Section: Discussionsupporting

confidence: 79%

“…have argued that the presence or absence of fever in SS depends on genetic susceptibility and is not an essential feature for the diagnosis of SS. These studies and many others confirm the highly variable nature of these criteria and suggest that their absence does not warrant ruling out the diagnosis of SS.…”

Section: Discussionmentioning

confidence: 72%

“…As evidenced by the available literature, the diagnosis of SS generally seems to be based on the aforementioned current criteria ; in some cases, however, the diagnosis is not as straightforward, potentially resulting in delayed diagnosis. Moreover, published reports show the absence of certain criteria as well as non‐inclusion of some emerging variants, thus highlighting the need for more precise diagnostic criteria .…”

Section: Introductionmentioning

confidence: 99%

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Sweet's syndrome: diagnostic criteria revisited

Nofal

Abdelmaksoud

Amer³

et al. 2017

J Deutsche Derma Gesell

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Summary The diagnosis of Sweet's syndrome (SS) is based on a set of criteria that requires the presence of two major and at least two minor criteria. In some cases, however, the diagnosis is not as straightforward due to the absence of certain criteria. The objective of the present study was to review the clinical, histopathological, and laboratory features of the current diagnostic criteria for SS, and to evaluate their validity in the cases reported in the literature as well as in 40 patients treated at our institution. Our comprehensive review of the current criteria for SS reveals that the two major criteria have been consistently present in all cases – including ours – since the first description of SS in 1964. With regard to the minor criteria, on the other hand, there has been marked variability between different studies, and many cases failed to fulfill the requirement of showing two minor criteria. In order to simplify the diagnosis, avoid misdiagnosis, and allow for prompt treatment, we propose two sets of revised diagnostic criteria for SS. The first set comprises constant clinical and histopathological features that must be present and are by themselves sufficient for the diagnosis of SS to be established. The second set includes variable features whose absence does not warrant ruling out SS.

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Section: Discussionsupporting

confidence: 79%

Section: Discussionmentioning

confidence: 72%

Section: Introductionmentioning

confidence: 99%

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Sweet's syndrome: diagnostic criteria revisited

Nofal

Abdelmaksoud

Amer³

et al. 2017

J Deutsche Derma Gesell

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“…Only three other papers reported Sweet syndrome as an initial presentation in adult SLE. [7][8][9] Sweet syndrome is an acute febrile neutrophilic dermatosis which often presents in idiopathic fashion can also be drug induced, associated with malignancy, or connective tissue diseases. 10 It is shown in Table 1.…”

Section: Discussionmentioning

confidence: 99%

Sweet syndrome: a sweet disease with a bitter diagnosis

et al. 2018

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Sweet syndrome is an acute febrile neutrophilic dermatosis first described by Robert Douglas Sweet in 1964. Sweet syndrome presents in three clinical settings: classical (or idiopathic), malignancy-associated, and drug-induced. It has been associated with hematopoietic malignancies and myelodysplastic disorders. A-28-years married woman presented to us with chief complaints of Fever and Multiple swellings over the body since 2 months. At presentation she has Pallor; venous hum present. Multiple, tender, erythematous subcutaneous swellings, firm in consistency noted in both forearms. Skin over the swellings is pinchable; superficial skin is normal. Sweet syndrome can occasionally cause an intense systemic response involving the lungs, liver and musculoskeletal system. The skin lesions in Sweet syndrome typically start as erythematous papules, plaques, and nodules. The lesions can take on pseudovesicular or pseudopustular appearance, and sometimes fully formed vesicles or pustules develop. The lesions can be subcutaneous mimicking erythema nodosum which can’t be differentiated unless a biopsy is taken. Because the diagnosis of Sweet syndrome can be challenging, particularly when associated with other connective tissue disorders such as SLE, a set of diagnostic criteria were proposed initially by Su and Liu and then revised by Von den Driesch. The diagnosis is based upon the presence of two major and two of the four minor criteria. Concurrent Sweet syndrome and SLE are exceedingly rare. Twelve patients with both Sweet syndrome and systemic lupus erythematosus (SLE) have been previously reported. We report a case of sweet syndrome associated with SLE diagnosed in our hospital. In our patient, diagnostic criteria are satisfied for Sweet syndrome as well as for SLE (ACR criteria-patient had polyarthralgia, anemia, thrombocytopenia, ANA and Ds DNA positive. Four out of 11 are fulfilled for SLE). Patient responded to corticosteroids.

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“…Außerdem zeigen die veröffentlichten Berichte, dass bestimmte Kriterien fehlen können und einige neue Formen nicht mit aufgenommen wurden. Dies unterstreicht die Notwendigkeit genauerer Diagnosekriterien .…”

Section: Introductionunclassified