“…A higher incidence of the disease in northern countries (about 60 per 100,000) than in southern European countries [ 5 ]. The disease is more common in women than men, nonsmokers than smokers, and in some races, such as African Americans, with familiar forms in less than 10% of cases [ 5 , 6 ].In France, mortality is estimated at 3.6 per million habitats, usually related to pulmonary fibrosis and respiratory failure [ 7 ].…”