Askin's tumor of the chest wall: A case report in an adult

Cabezali, Roger; Lozano, Ricardo; Bustamante, E.; Castiella, Tomás; Güemes, Antonio; Ramı́rez, José M.; Moncada, E.; Sousa, Ramón; Gil, Ismael

doi:10.1016/s0022-5223(94)70368-x

Cited by 11 publications

(6 citation statements)

References 5 publications

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“…Magnetic resonance imaging is advocated for knowing the extent of tumour extension into the chest wall and the lung [5].Tissue biopsy remains the most important diagnostic tool, with imaging modalities playing a complimentary role to delineate the extent of the disease before planning the treatment and for eventual follow up. Treatment includes surgical resection (if possible) followed by aggressive chemotherapy which produces excellent results as in case of Ewing Sarcoma/ PNET elsewhere [7].…”

Section: Discussionmentioning

confidence: 99%

Askin Tumour: A rare childhood thoraco -pulmonary malignancy of Ewing’s family of tumours

Mathur¹,

Jain²,

Singh³

et al. 2012

CMJ

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AbstactPrimitive neuro-ectodermal tumour of chest wall or the Askin tumour is a rare, malignant small cell neuroepithelioma that arises from the chest wall or lung. It is seen predominantly in children and adolescents. Although its appearance by light microscopy is similar to Ewing's sarcoma, rhabdomyosarcoma, neuroblastoma and lymphoma, which account for bulk of chest wall neoplasms in this age group, yet the Askin tumour is a distinct entity. We present a case of Askin tumour in a child, a rare malignant tumour in the thoraco-pulmonary area with highly aggressive clinical course.Keywords: Askin Tumour, primitive neuro-ectodermal tumour, malignant small cell neuroepithelioma ÖzetGöğüs duvarının primitif nöro-ektodermal tümörü veya diğer bir deyişle Askin tümörü nadir görülen bir küçük hücreli nöroepitelyoma olup göğüs duvarı veya akciğer kökenlidir. Ağırlıklı olarak çocuk ve adolesanlarda saptanır. Her ne kadar ışık mikroskopisindeki görünümü Ewing sarkomu, rabdomyosarkom, nöroblastom ve lenfoma gibi bu yaş grubunda çoğunlukla görülen göğüs duvarı neoplasmlarına benzese de Askin tümörü farklı bir antitedir. Bu makalede yüksek derecede agresif klinik seyirli, torakopulmoner alan yerleşimli nadir bir malignite olan Askin tümörlü bir çocuk hasta sunulmuştur.Anahtar sözcükler: Askin tümörü, primitif nöroektodermal tümör, malign küçük hücreli nöroepitelyoma Geliş tarihi

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Section: Discussionmentioning

confidence: 99%

Askin Tumour: A rare childhood thoraco -pulmonary malignancy of Ewing’s family of tumours

Mathur¹,

Jain²,

Singh³

et al. 2012

CMJ

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“…[ 6 ] Results of 123I-Tyr-3-Octeotride scintigraphy are positive for most of the tumors and metastasis. [ 7 ] Characteristics PENT pathologic findings include compact nests of small cells, Homer-Wright pseudo rosettes with an acidophilic core of neurofibrillar characteristics, and uptake of neuron specific enolase stain. [ 8 ]…”

Section: Discussionmentioning

confidence: 99%

Primitive neuro-ectodermal tumor of the lung in an adult

Gaude

Kangale

et al. 2009

Lung India

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“…Pertenecen a los tipos histológicos más indiferenciados de tumores malignos. Consisten en proliferación neoplásica de células pequeñas de núcleo redondo de pequeño o mediano tamaño, escaso citoplasma y múltiples mitosis con la formación características de rosetas de Homer-Wrigth (9,10) .…”

Section: Diagnósticounclassified

Sarcoma de Ewing costal

Tovar¹,

Parra²,

Villalón³

et al. 2021

Neumol Pediatr

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Los Sarcomas Ewing/PNET son altamente agresivos y ambos tumores presentan el mismo espectro de anomalías genéticas razón por la que se usa el término de “Tumores de la familia del sarcoma de Ewing (TFSE)” que abarca a un grupo de tumores con un espectro de diferenciación neuroectodérmica. Se presenta caso de adolescente femenina de once años, quien refirió dolor punzante, en hemitorax izquierdo, en Rx del tórax imagen densa heterogénea de bordes difusos proyectada sobre tercio medio basal en campo pulmonar izquierdo. Recibió antibióticos, permaneció asintomática hasta ocho meses después cuando reapareció dolor torácico, y en Rx del tórax se evidencio a nivel del octavo arco costal erosión ósea, además de la imagen anteriormente descrita de mayor tamaño. Examen físico y de laboratorios fueron normales, en Tomografía axial computarizada del tórax se evidencio erosión ósea, y compromiso de la pleura local. Biopsia de la lesión reportó: “Tumor maligno de células redondas, extensa necrosis”. Gammagrama Óseo señaló actividad osteoblástica alterada en D8 sugestivo de infiltración ósea secundaria. Se realizó resección de lesión tumoral, reconstrucción, colocación de prótesis, catéter central biopsia de Médula ósea: negativa. Los hallazgos morfológicos e inmunohistoquímicos con positividad para FLy y CD99 compatible con tumor de la familia del sarcoma de Ewing/tumor neuroectodérmico primitivo. Actualmente en tratamiento programado con quimioterapia estándar cada 21 días Radioterapia en la semana 12.

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Askin's tumor of the chest wall: A case report in an adult

Cited by 11 publications

References 5 publications

Askin Tumour: A rare childhood thoraco -pulmonary malignancy of Ewing’s family of tumours

Askin Tumour: A rare childhood thoraco -pulmonary malignancy of Ewing’s family of tumours

Primitive neuro-ectodermal tumor of the lung in an adult

Sarcoma de Ewing costal

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