Ascites as a Sole Presentation of Juvenile Granulosa Cell Tumor

Abstract

Granulosa cell tumors (GCT) are rare tumor and they constitute only 2% of all ovarian tumor. They are categorized in to juvenile and adult types. Juvenile Granulosa cell tumors only contribute to 5% of all GCT and they usually affect young children and premenarchal girls. These tumor are mainly hormone producing and mostly present with signs of precocious puberty. However other clinical presentation like acute abdomen or abdominal distention has also been reported. Here we present a 2 years old girl who reported to us with complaints of progressive abdominal distention and urinary retention. Her tumor markers were negative and her ultrasound and CT with contrast showed a massive abdominal ascites and complex ovarian mass. Exploration and left salpingoopherctomy with ascitic fluid sampling done. Her ascitic fluid was negative for tumor cell. To our knowledge it is a unique case in which stage 1A co-existed with ascites fluid negative of tumor cells.