Arrhythmogenic right ventricular dysplasia associated with atrioventricular conduction disturbance

Beerman, Lee B.; Zuberbuhler, James R.; Neches, William H.; Fischer, Donald R.; Fricker, Frederick J.; Mathews, Robert A.; Park, Sang C.; Lenox, Cora C.

doi:10.1016/0002-9149(83)90441-1

Cited by 7 publications

(2 citation statements)

References 6 publications

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“…In patients with AC and syncope beyond detectable or inducible monomorphic VT, several mechanisms of syncope could be identified with conduction disease as the predominant finding. 14) The autopsy findings have shown that specific RV wall abnormalities are associated primarily with His bundle 15) 16) and LV abnormalities. 16) In an autopsy study of 200 consecutive AC cases, the His bundle and its branches were abnormal in most cases (68%), either because of infiltration of adipose tissue (8%), fibrosis (54%), or both (6%).…”

Section: Discussionmentioning

confidence: 99%

Arrhythmogenic Noncompaction Cardiomyopathy: Is There an Echocardiographic Phenotypic Overlap of Two Distinct Cardiomyopathies?

Aras

Özeke

Çay

et al. 2015

J Cardiovasc Ultrasound

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The clinical diagnosis of right ventricular (RV) cardiomyopathies is often challenging. It is difficult to differentiate the isolated left ventricular (LV) noncompaction cardiomyopathy (NC) from biventricular NC or from coexisting arrhythmogenic ventricular cardiomyopathy (AC). There are currently few established morphologic criteria for the diagnosis other than RV dilation and presence of excessive regional trabeculation. The gross and microscopic changes suggest pathological similarities between, or coexistence of, RV-NC and AC. Therefore, the term arrhythmogenic right ventricular cardiomyopathy is somewhat misleading as isolated LV or biventricular involvement may be present and thus a broader term such as AC should be preferred. We describe an unusual case of AC associated with a NC in a 27-year-old man who had a history of permanent pacemaker 7 years ago due to second-degree atrioventricular block.

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Section: Discussionmentioning

confidence: 99%

Arrhythmogenic Noncompaction Cardiomyopathy: Is There an Echocardiographic Phenotypic Overlap of Two Distinct Cardiomyopathies?

Aras

Özeke

Çay

et al. 2015

J Cardiovasc Ultrasound

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“…A low incidence of ventricular fibrillation and sudden death has been reported (Marcus et al, 1982;Reiter er al., 1983), although a recent study suggests a higher propensity for ventricular fibrillation (Rowland et al, 1984). Atrioventricular conduction disturbances have only rarely been mentioned (Beerman et al, 1983;Bharati et al, 1978;Marcus et al, 1982).…”

Section: Discussionmentioning

confidence: 99%

Arrhythmogenic right ventricular dysplasia presenting with ventricular tachycardia in a father and son

B‐Lundqvist

Eneström

Edvardsson

et al. 1987

Clinical Cardiology

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A father and his son presented with ventricular tachycardia of left bundle-branch block configuration, two years apart. The patients had no clinical signs of right or left ventricular dysfunction. The diagnosis of arrhythmogenic right ventricular dysplasia was based on right ventricular angiographic and radionuclide findings. Microscopic sections obtained at surgery for the ventricular tachycardia in the father revealed abnormal infiltration of fat and focal fibrosis in the right ventricular myocardium, confirming the diagnosis. The importance of thorough evaluation of right and left ventricular function and structure in patients with ventricular tachycardia of right ventricular origin is emphasized. Currently available diagnostic techniques and management are presented.

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Inducible ventricular fibrillation in arrhythmogenic right ventricular dysplasia

Panidis

Greenspan

Mintz

et al. 1985

American Heart Journal

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Arrhythmogenic right ventricular dysplasia associated with atrioventricular conduction disturbance

Cited by 7 publications

References 6 publications

Arrhythmogenic Noncompaction Cardiomyopathy: Is There an Echocardiographic Phenotypic Overlap of Two Distinct Cardiomyopathies?

Arrhythmogenic Noncompaction Cardiomyopathy: Is There an Echocardiographic Phenotypic Overlap of Two Distinct Cardiomyopathies?

Arrhythmogenic right ventricular dysplasia presenting with ventricular tachycardia in a father and son

Inducible ventricular fibrillation in arrhythmogenic right ventricular dysplasia

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