Abstract:Normocephalic pancraniosynostosis is a rare form of craniosynostosis that usually presents later in life secondary to a delayed onset of symptoms and the presence of a normal head shape. Since its initial description in the literature in 2010, normocephalic pancraniosynostosis remains a rare clinical entity that has only been reported in 6 patients. Surgical treatment in the 2 published reports has been by staged total calvarial reconstruction or anterior cranial vault remodeling with bilateral frontoorbital a… Show more
Our reported case adds to the current limited knowledge of this rare entity and emphasized the importance of a high index of suspicion in children with apparently normal head size and shape but show subtle evidence of raised intracranial pressure.
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