Anomalous Origin of the Right Coronary Artery From the Pulmonary Artery: A Systematic Review

Guenther, Timothy M.; Sherazee, Elan A.; Wisneski, Andrew D.; Gustafson, Joshua D.; Wozniak, Curtis J.; Raff, Gary W.

doi:10.1016/j.athoracsur.2020.01.082

Cited by 48 publications

(70 citation statements)

References 33 publications

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“…According to previous review, about 38% of patients with ARCAPA were asymptomatic at the time of diagnosis. There is a bimodal distribution of the age at presentation as one peak centered near after birth and another peak centered around 40 to 60 years of age [5]. The reason for such phenomenon could be explained by the pathophysiology of ARCAPA.…”

Section: Discussionmentioning

confidence: 99%

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Surgical Treatment for Anomalous Origin of the Right Coronary Artery from the Pulmonary Artery: A Case Report with Five-Year Follow-up

Teng

2020

Preprint

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Background: Anomalous origin of the right coronary artery from the pulmonary artery (ARCAPA) is a rare congenital heart disease affecting about 0.002% of the population. Knowledge of ARCAPA is almost collected from case reports. The aim of this study was to provide a rare case to better understand this rare congenital coronary anomaly.Case presentation: We report a rare case of an 18-year-old male who was initially referred because of heart murmur. Dilated and tortuous coronary arteries were detected by echocardiography and congenital coronary anomaly was suggested. Further coronary CT angiography confirmed the diagnosis of ARCAPA. Although dual coronary system provides favorable long-term outcome, bypass surgery was considered technically difficult due to the huge mismatch of caliber between the right coronary artery and graft vessels. Eventually, simple right coronary artery ligation was performed. The patient was followed up for about 5 years without evidence of atherosclerosis or myocardial ischemia.Conclusions: ARCAPA presents as a rare congenital heart disease with variable clinical manifestations. Surgical treatment is highly recommended to re-establish dual coronary system and prevent further complications. To our best knowledge, only about 200 cases of ARCAPA has been reported.

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Section: Discussionmentioning

confidence: 99%

“…The embryological basis of ARCAPA remains unclear while it is generally thought with malformation of coronary artery development during the fourth to sixth week of gestation [4]. Aortopulmonary window is the most common cardiac lesions associated with ARCAPA, accounting for about one forth cases [5].…”

Section: Discussionmentioning

confidence: 99%

Surgical Treatment for Anomalous Origin of the Right Coronary Artery from the Pulmonary Artery: A Case Report with Five-Year Follow-up

Teng

2020

Preprint

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“…ARCAPA, though largely asymptomatic in nature, has been implicated in heart failure, myocardial ischemia, and sudden cardiac death. 2 Myocardial ischemia occurs as a result of flow reversal across the coronary artery into the pulmonary artery, as pulmonary vascular resistance and pulmonary artery pressure decreases after birth. 3 Unlike anomalous left coronary artery from pulmonary artery, ARCAPA appears to convey lower risk for heart failure.…”

Section: Discussionmentioning

confidence: 99%

“…Approximately one third of ARCAPA cases are associated with other congenital heart disease, most commonly aortopulmonary window. 2,4 Other associated defects included atrial and ventricular septal defects, bicuspid aortic valve, coarctation of the aorta, and patent ductus arteriosus. To date, this is the first case describing ARCAPA associated with partial anomalous pulmonary venous return.…”

Section: Discussionmentioning

confidence: 99%

Anomalous Right Coronary Artery off the Pulmonary Artery Strikes When You Least Expect It!

Voleti

Bukhari

Tongut

et al. 2021

CASE

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“…Various devices are being used to perform percutaneous transcatheter procedures like coils, umbrella devices, detachable balloons, vascular plugs, covered stents, and duct occluders. The recurrence rate after for about one-fourth of cases (29). It is clear that both CPAF and ARCAPA share some of the associated congenital heart diseases.…”

Section: Key Pointsmentioning

confidence: 97%

Congenital Coronary Artery–to–Pulmonary Artery Fistula with Anomalous Origin of Right Coronary Artery from Pulmonary Artery: A Case of “Double Trouble”

Kumar

2021

Radiology: Cardiothoracic Imaging

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Congenital coronary artery fistula is a rare coronary anomaly. Its clinical significance focuses mainly on the mechanism of coronary steal phenomenon. A combination of left main (LM) coronary artery-to-main pulmonary artery (MPA) fistula with anomalous origin of right coronary artery from the pulmonary artery (ARCAPA) was encountered in a 3-month-old infant who presented with tachypnea. Evaluation with echocardiography and CT confirmed the diagnosis. The patient underwent surgical ligation of LM-to-MPA fistula with direct reimplantation of ARCAPA to aortic root.

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Anomalous Origin of the Right Coronary Artery From the Pulmonary Artery: A Systematic Review

Cited by 48 publications

References 33 publications

Surgical Treatment for Anomalous Origin of the Right Coronary Artery from the Pulmonary Artery: A Case Report with Five-Year Follow-up

Surgical Treatment for Anomalous Origin of the Right Coronary Artery from the Pulmonary Artery: A Case Report with Five-Year Follow-up

Anomalous Right Coronary Artery off the Pulmonary Artery Strikes When You Least Expect It!

Congenital Coronary Artery–to–Pulmonary Artery Fistula with Anomalous Origin of Right Coronary Artery from Pulmonary Artery: A Case of “Double Trouble”

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