Anomalous origin of the right coronary artery from the pulmonary artery associated with an aortopulmonary window

Bhat, Padebettu Subramanya Seetharama; Chandrashekar, Chandana Nirmala; Mallikarjun, Divya; Gowda, S L Girish

doi:10.4103/apc.apc_65_18

Cited by 6 publications

(4 citation statements)

References 6 publications

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“…Although this was previously reported in the setting of aortopulmonary window and tetralogy of Fallot. 2 , 3 , 4 , 5 A similar case was noted in a previous ARCAPA case series published in 2006, 5 in a patient with tetralogy, pulmonary atresia with right pulmonary artery off the descending aorta, and left pulmonary artery off the ascending aorta. This patient was diagnosed with ARCAPA intraoperatively following RCA ligation and died on the first postoperative day.…”

Section: Discussionsupporting

confidence: 68%

ARCAPA in Pulmonary Atresia, Ventricular Septal Defect, and Major Aortopulmonary Collateral Arteries

McCay,

Ramanayake,

Bates

et al. 2024

JACC: Case Reports

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Section: Discussionsupporting

confidence: 68%

ARCAPA in Pulmonary Atresia, Ventricular Septal Defect, and Major Aortopulmonary Collateral Arteries

McCay,

Ramanayake,

Bates

et al. 2024

JACC: Case Reports

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“…4 Anomalous origin of the right coronary artery from the pulmonary artery (ARCAPA) associated with the aortopulmonary window is a very rare entity, with few reported cases in the literature. 5 ARCAPA is extremely rare with an incidence of 0.002% in the general population. 6 Sixty-six per cent of the cases of ARCAPA are associated with other congenital disorders such as aortopulmonary window, tetralogy of Fallot, ventricular septal defect, and aortic stenosis.…”

Section: Discussionmentioning

confidence: 99%

Aortopulmonary window with anomalous right coronary artery from the pulmonary artery. Case report and literature review

et al. 2019

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Aortopulmonary window is a rare congenital heart lesion. It might be associated with other CHDs, as well as with anomalous origin of the coronary arteries. Anomalous origin of the right coronary artery from the pulmonary artery (ARCAPA) is the most commonly described coronary artery anomaly in association with aortopulmonary window. We are describing a premature neonate who was diagnosed to have aortopulmonary window and ARCAPA immediately after birth, and had a successful operation at the age of 4 months. This report highlights the importance of very careful assessment of the coronary arteries in patients with aortopulmonary window.

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“…This coronary anomaly association with APW is extremely rare. It was reported in 1999 by Izumoto et al, and recently in Padebettu et al [16,17].…”

Section: Discussionmentioning

confidence: 79%

Aortopulmonary Window: Types, Associated Cardiovascular Anomalies, and Surgical Outcome. Retrospective Analysis of a Single Center Experience

Bin-Moallim

Hamadah

Alhabshan

et al. 2020

Journal of the Saudi Heart Association

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Objective: Aortopulmonary window (APW) is a rare congenital heart defect. It occurs as an isolated cardiac lesion or in association with other cardiac anomalies and rarely with abnormal coronary arteries. The spectrum of cardiovascular anomalies associated with APW and overall management and outcome in the current era were reviewed. Methods: Between 2001 and 2018, all patients diagnosed with APW were included. Based on associated cardiovascular anomalies, those patients were divided into 2 groups: simple APW group and complex APW group (APW with associated other cardiovascular anomalies). All cases were followed longitudinally. The outcomes are described. Result: Twenty patients underwent APW repair including 2 (10%) in simple APW group and 18 (90%) in complex APW group. Their mean age and weight were 4.8 ± 1.8 months and 4 ± 0.4 kg, respectively. APW Type I was confirmed in 65% followed by Type III in 20% and then Type II in 15% of the patients. In the complex APW group, atrial septal defect was the commonest associated cardiac lesion occurring in 8/20 (40%), followed by ventricular septal defect, interrupted aortic arch, and pulmonary artery anomalies in 25% of each. The presence of patent ductus arteriosus (PDA) was found in 40% of APW cases with 2/3rd of them in association with interrupted aortic arch. Two patients (10%) had unusual coronary anomalies that required repair, both with APW Type I. Associated non-cardiac anomalies were found in 30% of cases. Risk Adjustment for Congenital Heart Surgery (RACHS-1) score frequencies were between 2 and 4. Only one patient had reactive pulmonary hypertension related to chronic lung disease. All patients underwent surgical correction with median age of 2 month at the time of repair (interquartile range, 2 weeks to 4.5 months). Mean duration of mechanical ventilation, pediatric cardiac ICU and hospital length of stay were 2.8 ± 0.5, 9 ± 3 and 26 ± 6 days, respectively. All patients survived with no residual APW with mean follow-up duration of 4.5 years. Conclusion: Majority of APW are associated with other cardiovascular anomalies (90%) including coronary abnormalities (10%). Early surgical repair of APW and associated lesions showed excellent survival rate, freedom from re-intervention need within an average of 4.5 years of follow up and no evidence of persistent pulmonary hypertension post repair.

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Anomalous origin of the right coronary artery from the pulmonary artery associated with an aortopulmonary window

Cited by 6 publications

References 6 publications

ARCAPA in Pulmonary Atresia, Ventricular Septal Defect, and Major Aortopulmonary Collateral Arteries

ARCAPA in Pulmonary Atresia, Ventricular Septal Defect, and Major Aortopulmonary Collateral Arteries

Aortopulmonary window with anomalous right coronary artery from the pulmonary artery. Case report and literature review

Aortopulmonary Window: Types, Associated Cardiovascular Anomalies, and Surgical Outcome. Retrospective Analysis of a Single Center Experience

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