Anomalous origin of one pulmonary artery from the ascending aorta

Abstract

Although operative survival is now possible for this malformation, reports of late results are lacking. Two of the three patients developed stenosis at the surgical anastomosis relatively early after surgery. Larger numbers of operations are necessaries to reach definitive conclusions.

Interim prostacyclin therapy for an isolated disconnected pulmonary artery: a case report

“…Our patient was in an unusual situation, in that this anomaly was not associated with conotruncal anomalies [1], as described in association with fetal valproate syndrome [6]. Moreover, our patient responded well to an epoprostenol infusion.…”

“…Disconnected pulmonary arteries are unusual, and are almost invariably associated with conotruncal abnormalities [1]. We report a three-month-old infant who presented in heart failure and severe pulmonary hypertension due to a disconnected right pulmonary artery in the absence of conotruncal anomalies.…”

Anomalous origin of one pulmonary artery from the ascending aorta (hemitruncus) in a premature infant: A case report and literature review

“…1 Early diagnosis is essential, so that early surgical repair can be performed to improve outcome. [3][4][5][6][7][8] Their gestational age, birth weight, diagnosis, diagnostic tools, age at diagnosis, associated anomalies, age at surgery, and outcome are reported in Table 1. Early diagnosis may be missed because of nonspecific findings of clinical symptoms, chest radiography, and electrocardiogram.…”

“…3 However, many factors may contribute to the delay in diagnosis and surgical repair of this cardiac anomaly. [3][4][5][6][7][8] Some authors have suggested that this malformation should be suspected during echocardiographic examination in patients with signs of congestive heart failure and pulmonary hypertension without structural intracardiac defects. 1 In premature infants, early diagnosis may be even more difficult.…”

A rare anomaly: 'hemitruncus'

“…Hemitruncus is best defined as a condition in which one branch of the pulmonary artery originates from the ascending aorta and the other branch of the pulmonary artery courses normally from the main pulmonary artery which arises from the right ventricle 1 2. The anomalous origin of one pulmonary artery from the ascending aorta should be suspected when unexplained pulmonary hypertension is diagnosed and no structural intracardiac defects are observed.…”