Anomalous Coronary Arteries

Invasive Coronary Assessment in a 9-Year-Old With Anomalous Aortic Origin of the Left Coronary Artery

“…The procedure and follow-up management were uncomplicated. 3 At three months postoperatively, DSCMR again showed no perfusion defects. The CTA showed a normal LCA ostium now arising from the left sinus of Valsalva with no intramural course and an 8 mm residual interarterial course (Figure 1C and D).…”

“…Congenital coronary anomalies represent about 1% of the general population and are the second leading cause of sudden cardiac death in the young. [1][2][3] High-risk subtypes include those with intramural or interarterial course, especially anomalous aortic origin of the left coronary artery (AAOLCA). We demonstrate the utility of invasive coronary assessment under provocative stress in a nine-year-old boy with AAOLCA.…”

High-Risk Anomalous Aortic Origin of the Left Coronary Artery: Consecutive Admissions Presenting With Sudden Cardiac Arrest

“…5 However, echocardiography can correctly diagnose up to 95% of patients. 1 This suggests the importance of exhaustive evaluation of exertional syncope or chest pain to exclude congenital coronary anomalies. 1,5 Advanced evaluation of affected patients with CT angiography is also of high diagnostic yield, with evaluations demonstrating 100% accuracy in demonstrating the anomalous origin of coronary arteries.…”

“…1 This suggests the importance of exhaustive evaluation of exertional syncope or chest pain to exclude congenital coronary anomalies. 1,5 Advanced evaluation of affected patients with CT angiography is also of high diagnostic yield, with evaluations demonstrating 100% accuracy in demonstrating the anomalous origin of coronary arteries. 6 This modality is particularly useful in risk stratification and surgical planning as it offers optimal visualization of the extent of the intramural or interarterial course of the vessel, as well as ostial morphology.…”

Classification, diagnosis and clinical strategy of congenital coronary artery disease in children

“…Intermural couse means the anomalous coronary artery from the aorta is usually with an acute angle takeoff, which will lead to Slit-like/fish-mouth-shaped orifice. It is postulated that exercise results in the expansion of the aorta, which occludes the acutely angulated slit-like orifice of the coronary artery (29)(30)(31)(32). At present, there are many inferences about the mechanism of ACAOS complicated with sudden death during inter-arterial course.…”