Angiomiolipoma renal múltiple bilateral asociado a esclerosis tuberosa. Reporte de caso y revisión de la literatura

An approach to the tuberous sclerosis complex

“…Renal angiomyolipoma is a rare benign mesenchymal neoplasm characterized by the presence of thin dysmorphic veins, smooth muscle in variable proportion and adipose tissue, presenting associated with tuberous sclerosis, associated with TSC1 and TSC2 with frequency of 65 to 80% of patients studied by ultrasound, with a predilection for the female sex from 2 to 1; it can be asymptomatic or present with symptoms such as flank pain, hematuria or Wunderlich syndrome, characterized by hypovolemic shock associated with flank pain with perirenal hematoma. 21,49…”