V ena cava superior syndrome (VCSS) is a clinical picture emerging with the impairment of blood flow and venous return to the heart as a result of the obstruction of superior vena cava. Depending on the acutely developing obstruction of blood flow, respi-ratory distress and neurologic symptoms arise [1]. VCSS was first described by William Hunter in 1757 in a patient with syphilitic aorta aneurism. Vena cava syndrome in children develops as a result of external pressure depending on the oncologic problems. VCSS ABSTRACT OBJECTIVE: Vena cava superior syndrome comprises various symptoms of compression of vena cava superior. The results of increased venous pressure in the upper body may cause edema of the head and neck associated with cyanosis, plethora and distended subcutaneous vessels. Vena cava superior syndrome is rare in childhood. Therefore, we planned this retrospective study.