Anesthetic management of a patient with Bartter′s syndrome undergoing bilateral sagittal split osteotomy

Abstract

Bartter's syndrome is an unusual (estimated incidence is 1.2 per million people) but important congenital form of secondary hyperaldosteronism; due to abnormalities in renal handling of electrolytes. It is associated with hypertrophy and hyperplasia of the juxtaglomerular cells, normal blood pressure, and hypokalemic alkalosis withoutedema.We present a 22-year-old woman with Bartter's syndrome underwent bilateral sagittal split osteotomy to correct mandibular prognathic. The anesthetic management of Bartter's syndrome should be relevant to the pathophysiology of the syndrome. Therefore, it should be directed toward maintaining cardiovascular stability, control of associated fluid, electrolyte and acid–base derangements, and the prevention of renal damage.

Anaesthetic Management for Hiatal Hernia Repair in a Child with Bartter's Syndrome: A Case Report

“…Bartter syndrome is an autosomal recessive disorder with an estimated worldwide incidence of 1.2 per million people. 1 It is an inherited tubulopathy characterized by markedly reduced sodium chloride transport in the distal nephrons. Although general review literature is available on pathogenesis, clinical manifestations and management but there are no controlled trials and only few case reports due to its low prevalence.…”