Anesthetic Management of a Parturient with Myotonia Atrophica

Hook, Robert; Anderson, Edward F.; Noto, Phillip

doi:10.1097/00000542-197512000-00022

Cited by 26 publications

(3 citation statements)

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“…There is an increased incidence of spontaneous abortion, premature and prolonged labour. The uterus is often atonic with poor uterine contraction, and postpartum haemorrhage requiring hysterectomy has been reported [48].…”

Section: The Clinical Syndromes (Table Ii) [92]mentioning

confidence: 99%

Anaesthesia and myotonia

Russell

Hirsch

1994

British Journal of Anaesthesia

119

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Myotonia is an intrinsic disorder of muscle, and not of the peripheral nerve or neuromuscular TABLE I. The myotonias Myotonic dystrophy (dystrophia myotonica, myotonia atrophies, Steinert's disease) Myotonia congenita (Thomsen's disease) "Classical" Thomsen's disease Myotonia fluctuans Acetazolamide responsive myotonia congenita Recessive generalized myotonia (Becker's) Paramyotonia congenita Hyperkalaemic periodic paralysis (adynamia episodica heredita) Acid-maltase deficiency (Pompe's disease) Schwartz-Jampel syndrome (chondrodystrophic myotonia)

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Section: The Clinical Syndromes (Table Ii) [92]mentioning

confidence: 99%

Anaesthesia and myotonia

Russell

Hirsch

1994

British Journal of Anaesthesia

119

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“…Events similar to malignant hyperthermia (MH) may occur in patients with myotonia when they are exposed to volatile anaesthetics [1][2][3][4][5][6][7][8][9][10][11]. Moreover, depolarizing neuromuscular blocking drugs may cause masseter spasm or generalized muscle spasms in these patients and thus affect tracheal intubation or ventilation [1,[12][13][14][15][16][17][18][19][20][21][22].…”

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confidence: 99%

Are Myotonias and Periodic Paralyses Associated With Susceptibility to Malignant Hyperthermia?

Lehmann‐Horn¹,

Iaizzo

1990

British Journal of Anaesthesia

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Excised muscles from patients with myotonia or periodic paralysis were subjected to the in vitro contracture test for susceptibility to malignant hyperthermia (MH). In a group of 44 patients, this standard test gave four positive, 10 equivocal and 30 negative results. The results for 27 control muscles from normal subjects were negative. When the test was performed with less than normal concentrations of contracture-triggering substances (caffeine less than or equal to 2 mmol litre-1, less than or equal to 2% halothane), 70% of the muscles from the patients and only 15% of the controls responded with small contractures (less than 0.2 g). These results should not be taken to indicate that the patients have the genetic trait for MH. The positive and equivocal test results, in addition to the slight contractures, may be accounted for by the electrical after-activity in the cases of pure myotonia, and by increased resting myoplasmic [Ca2+] in myotonic dystrophy. This shows that the in vitro contracture test lacks specificity.

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“…Epidural (41,42), caudal (6,43) and spinal anaesthesia (44) have all been used successfully in patients with myotonic dystrophy without any untoward effects. If opioids are to be added to the local anaesthetic solution, then the risk of respiratory depression clearly still exists.…”

Section: Maintenancementioning

confidence: 99%

Myotonic dystrophy and paediatric anaesthesia

White

Bass

2003

Pediatric Anesthesia

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Myotonic dystrophy is a neuromuscular condition inherited in an autosomal dominant fashion, and is most commonly diagnosed in the neonatal period. With improving levels of care, these patients are now presenting more commonly for anaesthesia. We review the clinical features of the condition, and then discuss the steps in the anaesthetic process, outlining the anaesthetic implications of myotonic dystrophy at each stage.

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Anesthetic Management of a Parturient with Myotonia Atrophica

Cited by 26 publications

References 0 publications

Anaesthesia and myotonia

Anaesthesia and myotonia

Are Myotonias and Periodic Paralyses Associated With Susceptibility to Malignant Hyperthermia?

Myotonic dystrophy and paediatric anaesthesia

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