Anesthetic management in a patient with osteogenesis imperfecta for rush nail removal in femur

Abstract

Osteogenesis imperfecta (OI) is a rare genetically inherited syndrome involving connective tissues, resulting in anatomic and physiologic abnormalities, which results in any form of anesthesia, a challenging task. We hereby report a case of OI type I presented with distinctively blue sclera, hearing loss, kyphoscoliosis, and mild pulmonary restrictive disease who underwent rush nail removal in the femur.

Spinal Instead of General Anesthesia for Two Pediatric Patients at Risk for Malignant Hyperthermia

“…Our second patient highlights another benefit of spinal anesthesia as he required no postoperative analgesic or sedation medications, and therefore was discharged rapidly from the PACU to the phase two recovery area. Previous reports of the use of spinal anesthesia in MH susceptible adult patients are outlined in Table 1 [17][18][19][20][21][22][23]. Adverse effects were rare with hypotension noted in one parturient and respiratory difficulties in another patient related to a high spinal block (T3) and the concomitant administration of dantrolene.…”

“…Purohit [23] Adolescent female with osteogenesis imperfecta, considered at risk for MH, presenting for femoral nail removal.…”

Total Hip Replacements in Patients with Rare Pathologic Conditions Affecting Bone

“…In those with cervical spine instability, intubation for anesthesia has been performed under fiber-optic control 64 . Although spinal anesthetic is an alternative that has been utilized, substantial kyphoscoliosis deformity may make this option impractical 69 .…”

Rush Rodding of Femur in a Child with Osteogenesis Imperfecta Under Caudal Anaesthesia and Sedation: A Case Report

“…1 The disease is characterised by fragile bones, hyperextensible joints, blue sclera, improper dentition, and progressive hearing loss. 2 OI is classified into four types according to silence classification. 3 We present a known case of osteogenesis imperfect posted for rush rodding of femur successfully managed using caudal anaesthesia and sedation using dexmedetomidine infusion.…”