Anatomical repair of congenitally corrected transposition in the fifth decade of life

Baruah, Sudip Dutta; Marwah, Ashutosh; Dalvi, Bharat; Sharma, Rajesh

doi:10.1016/j.ihj.2016.02.024

Cited by 3 publications

(2 citation statements)

References 5 publications

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“…In a previous report, an adult patient with a similar anatomic arrangement, necessarily underwent anatomic repair because of severe systemic (tricuspid) AV valve regurgitation. 9 However, in the aforementioned case, the clinical picture was dominated by heart failure and congestion due to systemic ventricle dilatation and tricuspid regurgitation. In our patient, the key clinical and anatomic features were severe cyanosis, caused by severe pulmonary stenosis with hypertrophic not dilated ventricles.…”

Section: Discussionmentioning

confidence: 96%

A case report of late physiologic repair of congenitally corrected transposition of the great arteries and pulmonary stenosis in a severely cyanotic patient: better late than never

Ferrero

Chessa

Varrica

et al. 2021

European Heart Journal - Case Reports

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Background Patients with congenitally corrected transposition of great arteries (ccTGA) not infrequently seek medical attention for the first time late in life. Optimal management of natural history ccTGA is debated and must be tailored. Case summary A 38 years old male patient was referred to our centre because of severe cyanosis and worsening dyspnoea. Investigations disclosed: situs solitus, mesocardia, double discordance, large ventricular septal defect (VSD), severe pulmonary stenosis, no significant atrioventricular valves regurgitation. The patient underwent physiologic repair: VSD closure, placement of a left ventricle to pulmonary artery conduit and epicardial atrio-biventricular pacemaker implantation. The conduit was intentionally undersized to promote tricuspid valve continence. Postoperative course was uneventful, trans-thoracic echocardiography showed good biventricular function without significant tricuspid regurgitation. At one month after discharge the patients is in NYHA class II. Discussion Management of late presenter patients with ccTGA depends on the associated lesion and estimation of surgical risk. In selected patients markedly symptomatic physiologic repair is a rationale option, providing a normal saturation and biventricular circulation with a significantly lower surgical risk as compared with anatomic repair.

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Section: Discussionmentioning

confidence: 96%

A case report of late physiologic repair of congenitally corrected transposition of the great arteries and pulmonary stenosis in a severely cyanotic patient: better late than never

Ferrero

Chessa

Varrica

et al. 2021

European Heart Journal - Case Reports

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“…In 2016, Baruah reported performing a successful atrial switch plus a Rastelli operation in a 51-year-old patient with large VSD, severe PS, and severe TR. This patient, temporarily paced soon after surgery, had a good recovery, and was New York Heart Association class I at three months after operation [ 62 ] . Recently, Da Silva (personal communication) did a pulmonary root translocation plus a Senning procedure in a 46-year-old symptomatic patient with good RV function who had large VSD, moderate PS, and severe TR with good early follow-up.…”

Section: Managementmentioning

confidence: 99%

Congenitally Corrected Transposition of the Great Arteries in the Adult

Amaral¹,

Valente²,

Manso³

et al. 2022

Braz J Cardiovasc Surg

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Introduction Congenitally corrected transposition of the great arteries (CCTGA) is a rare anomaly. Current data available regarding adult cases is derived from small series, information simultaneously presented in pediatric publications, and one classical multicenter study. This review, not aimed to exhaust the subject, has the purpose to examine the literature addressing presentation, diagnostic methodology, and management of afflicted adult patients. Methods A comprehensive search was undertaken in three major databases (PubMed, Cochrane, SciELO), using the keywords “congenitally corrected transposition of the great arteries” and “adults”. Relevant articles in English, Spanish, and Portuguese were extracted and critically appraised in this review. Steps for study selection were: (1) identification of titles of records through databases searching, (2) removal of duplicates, (3) screening and selection of abstracts, (4) final inclusion in the study. Results Four hundred sixty-five publications on CCTGA in adult patients were retrieved, and 166 were excluded; 299 studies were used for this review including 76 full-text articles, 70 studies related to general aspects of the subject, and, due to the small number of publications, 153 case reports. Sixty-one articles referring to combined experiences in pediatric and adult patients and judged to be relevant, but retrieved from another sources, were also included. Conclusion Albeit clinical presentation and diagnostic criteria have been well stablished, there seems to be room for discussion related to clinical and surgical management of CCTGA in adults. Considering the rarity of the disease, well designed multicenter studies may provide answers.

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Congenitally Corrected Transposition of the Great Arteries

Karl

Jacobs

2023

Pediatric Cardiac Surgery

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Anatomical repair of congenitally corrected transposition in the fifth decade of life

Abstract: Successful repair of congenitally corrected transposition with ventricular septal defect and pulmonary stenosis presenting with heart failure in the fifth decade of life is described. This is the oldest patient to undergo this surgery, as per existing literature.

Cited by 3 publications

References 5 publications

A case report of late physiologic repair of congenitally corrected transposition of the great arteries and pulmonary stenosis in a severely cyanotic patient: better late than never

A case report of late physiologic repair of congenitally corrected transposition of the great arteries and pulmonary stenosis in a severely cyanotic patient: better late than never

Congenitally Corrected Transposition of the Great Arteries in the Adult

Congenitally Corrected Transposition of the Great Arteries

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