Arnold-Chiari malformation is a group of deformities seen in the hindbrain that is cerebellum, pons, and medulla oblongata. Based on the morphology of the malformations as seen radiologically or during an autopsy, Chiari II includes brainstem, fourth ventricle, and greater than 5 mm descent of the caudal tip of cerebellar tonsils past the foramen magnum with spina bifida. In the present case, a report of anesthetic management of a 29-year-old school clerk presented with hydrocephalus and myelomeningocele and MR imaging revealed herniation of cerebellum and medulla through foramen magnum, hence, confirming it to be a case of type II Chiari malformation posted for ventriculoperitoneal shunting and foramen magnum decompression.