“…Many surgical procedures have been described, including excision of the distal ulna (Nielsen, 1977;Ranawat et al, 1975;Schmidt-Rohlfing et al, 2001), ulnar shortening osteotomies (Bruno et al, 2003;Nielsen, 1977;Schmidt-Rohlfing et al, 2001), wrist denervation (Schmidt-Rohlfing et al, 2001), radiocarpal arthrodesis combined with distal ulna excision (Henry and Thorburn, 1967), Sauve´-Kapandji procedure (Angelini et al, 1996), epiphysiodesis (Vickers and Nielsen, 1992), opening or closing wedge osteotomy of the distal radius (De Paula et al, 2006;Houshian et al, 2000;Murphy et al, 1996, Schmidt-Rohlfing et al, 2001, or a combination of the above (Burrows, 1937;Dos Reis et al, 1998;Nielsen, 1977;Ranawat et al, 1975;Salon et al, 2000;Watson et al, 1993;White and Weiland, 1987). Due to the rarity of the condition, few studies in the literature describe more than 15 patients.…”