An interesting case of Herlyn–Werner–Wunderlich syndrome

Tigga, Maureen Prativa

doi:10.4103/tcmj.tcmj_13_19

Cited by 5 publications

(6 citation statements)

References 7 publications

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“… 4 Common presenting symptoms include increasing pelvic pain and dysmenorrhea following menarche. 5 In our case the symptoms appeared four years after menarche instead of following the typical pattern of symptom presentation soon after achieving menarche.…”

Section: Introductionmentioning

confidence: 51%

Herlyn-Werner-Wunderlich Syndrome: A Case Report

Lamichhane,

Sutihar,

Janakyraman

et al. 2023

J Nepal Med Assoc

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Herlyn-Werner-Wunderlich syndrome is a rare congenital malformation of the Mullerian ducts characterized by uterine didelphys with obstructed hemivagina and ipsilateral renal agenesis. Commonly, such patients present with pelvic pain, dysmenorrhea following menarche, and an abdominal mass secondary to hematometrocolpos. In this report, a case of a 14-year-old female presented with abdominal pain, back pain and acute urinary retention. She attained menarche at the age of 10 years; however, symptoms of dysmenorrhea only appeared 4 years later. She was eventually diagnosed with the help of ultrasound and computed tomography urogram. She was managed conservatively with an incision and drainage procedure and was also advised for resection of vaginal septum. The nonspecific nature of symptoms such as regular menstruation with cyclical abdominal pain impedes the diagnosis which can lead to an array of complications. Awareness of this syndrome can help avoid misdiagnosis and allow for early surgical intervention.

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Section: Introductionmentioning

confidence: 51%

Herlyn-Werner-Wunderlich Syndrome: A Case Report

Lamichhane,

Sutihar,

Janakyraman

et al. 2023

J Nepal Med Assoc

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“…The common presentations are dysmenorrhea, pelvic and abdominal pain due to hemotocolpos as a result of obstructed hemivagina 9 . Symptoms depends on the class of the syndrome.…”

Section: Discussionmentioning

confidence: 99%

Incidental diagnosis of Herlyn-Werner-Wunderlich Syndrome in a nulliparous woman: a case report in Bhutan

Sonam¹,

Pradhan²,

Tshomo³

2021

Bhutan Health Journal

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Herlyn-Werner-Wunderlich syndrome (HWWS) is a rare congenital syndrome with features of uterus didelphys, ipsilateral absent kidney and obstructed hemivagina. Ultrasound findings of absent kidney or abnormalities in the kidney should alert the clinicians about the syndrome. Complications like endometriosis, infertility and pelvic inflammation occurs with late diagnosis.A 42-yearold nulliparious married woman who presented with right sided abdominal pain to the National Referral Hospital was diagnosed to have HWWS. The diagnosis was supported by ultrasound, CT and MRI findings. Patient was treated for endometriosis and had symptomatic improvement. The diagnosis of the syndrome is challenging as it is rare but clinicians should suspect the syndrome in women who present with infertility. Ultrasound scan is the basic investigation to screen the syndrome which is available in most hospitals.

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“…Laboratory examinations have revealed that some patients have elevated levels of CA-199 [7] or CA-125 [16] . In this study, both patients showed elevated levels of CA-125 and 1 patient showed elevated level of CA-199, which returned to normal at the postoperative follow-up.…”

Section: Discussionmentioning

confidence: 99%

Herlyn–Werner–Wunderlich syndrome and its complications: A report of two cases and literature review

Li¹,

Liu²,

Li³

2021

Radiology Case Reports

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Herlyn–Werner–Wunderlich syndrome (HWWS) is a rare congenital malformation characterized by uterus didelphys, unilateral blind hemivagina, and ipsilateral renal agenesis. The obstructed vagina affects menstrual flow, leading to related clinical symptoms after menarche. However, the age of onset, initial symptoms, and clinical complications differ among patients owing to the different types of vaginal septum. Herein, we report 2 cases. The first case is of a 20-year-old woman who presented with fever; she was diagnosed with vaginitis and pelvic inflammation due to the vaginal septum with ostiole. The second case is of a 12-year-old girl who complained of abdominal pain; she was diagnosed as having pelvic inflammation, omentitis, and suppurative appendicitis due to the atretic vaginal septum.

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An interesting case of Herlyn–Werner–Wunderlich syndrome

Cited by 5 publications

References 7 publications

Herlyn-Werner-Wunderlich Syndrome: A Case Report

Herlyn-Werner-Wunderlich Syndrome: A Case Report

Incidental diagnosis of Herlyn-Werner-Wunderlich Syndrome in a nulliparous woman: a case report in Bhutan

Herlyn–Werner–Wunderlich syndrome and its complications: A report of two cases and literature review

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