An Autopsy Case of Primary Biliary Cirrhosis with Severe Interstitial Pneumonia.

Esophagogastric varices as a prognostic factor for the determination of clinical stage in patients with primary biliary cirrhosis

“…During the observation period, 9 (10.7%) of 84 patients died. There were 6 patients with liver-related death (3 with liver failure; 2 with variceal bleeding; and 1 with cholangiocellular carcinoma) and 3 patients with liver-unrelated death (hemorrhagic gastric ulcer, malig- nant melanoma, and interstitial pneumonia with rheumatoid arthritis 12 ). All liver-related deaths and the death due to hemorrhagic gastric ulcer occurred in s-PBC patients, while the death due to malignant melanoma and the death due to interstitial pneumonia with rheumatoid arthritis occurred in patients with a-PBC.…”

Successful treatment of primary Sjogren’s syndrome complicated with primary biliary cirrhosis and lung involvement

“…On the other hand, one of the most common (25% of LIP cases) associations of LIP is with pSS (3). There are isolated case reports in the literature demonstrating the association between SS secondary to rheumatoid arthritis, PBC and interstitial pneumonia (8,9). However, to our knowledge, a patient with pSS complicated with both PBC and LIP has not been reported before.…”

Hepatopulmonary Syndrome in a Patient with Primary Biliary Cirrhosis

“…Various therapeutic options, such as treatment with a somatostatin analogue (4), N(G)-nitro-L-arginine methyl ester (L-NAME) (13), aspirin (14), and other drugs have been tried for HPS patients, but no clear therapeutic effect of these drugs has been established. Hence, liver transplantation is the most effective current therapy for patients with mild to moderate HPS.…”