An atypical case of idiopathic retinal vasculitis, aneurysms, and neuroretinitis (IRVAN) syndrome

Abstract

Figure 3 The tied-knot-like sacculations were better visualized with indocyanine green angiography because of the lack of dye leakage with this method.Correspondence

Primary Branch Retinal Artery Occlusion in Idiopathic Retinal Vasculitis, Aneurysms, and Neuroretinitis Syndrome Associated With Hyperhomocysteinemia

“…4 Based on the findings of exudative retinopathy, arterial macroanuerysms, nonperfusion of peripheral capillaries, diffuse staining of the optic nerve head in late fundus fluorescein angiography (neuroretinitis), and mild uveitis, diagnosis of IRVAN syndrome was made in this healthy young man. Idiopathic retinal vasculitis, aneurysms, and neuroretinitis syndrome affects the retinal and optic disk vasculature and also the choroidal circulation in some cases.…”

Single Bilateral Dexamethasone Implant in Addition to Panretinal Photocoagulation and Oral Azathioprine Treatment in IRVAN Syndrome

“…These options include medical treatment, laser photocoagulation and vitreoretinal surgery, or a combination of them [2, 4, 5, 6, 7, 8, 9, 10, 11, 12, 13, 14, 15, 16]. …”

“…PRP is often effective, especially in disease stages 2 and 3 [5, 6, 7, 12]. The role of immunosuppressives or immunomodulatory treatment remains uncertain [2].…”

Rapid Regression of Exudative Maculopathy in Idiopathic Retinitis, Vasculitis, Aneurysms and Neuroretinitis Syndrome after Intravitreal Ranibizumab

“…Although the best therapy has not yet been established, RP seems to be the most suitable option to control the disease and to prevent its progression [1, 2, 3]. Other treatments have been reported with variable results such as corticosteroids [1, 2, 3], pars plana vitrectomy [2, 5], anti-TNF alpha agents [6], antiangiogenic drugs [7, 8] or the direct application of laser on aneurysms [9]. …”