Alveolar soft part sarcoma of the retroperitoneum: A case report

Abstract

Alveolar soft part sarcoma is a rare soft tissue tumor with uncertain histogenesis. It is a slow growing tumor with a high rate of metastasis. The tumor is not easily identified as clinical symptoms are not pronounced. The retroperitoneum is a rare location of tumor, with a few cases published in literature. Surgical excision is the mainstay of treatment. Here we describe a rare case of a large retroperitoneal Alveolar soft part sarcoma in a young female with radiological and histopathological findings.

PEComa of the Adrenal Gland

“…ASPS, another mesenchymal neoplasm of uncertain differentiation, may occasionally resemble PEComa. Clinically, ASPS also has a wide anatomic distribution but arises less commonly at visceral sites 23 . Histologically, ASPS is classically characterized by epithelioid cells with a strikingly organoid/nested or pseudo-alveolar growth pattern surrounded by prominent vasculature 24 .…”

“…Clinically, ASPS also has a wide anatomic distribution but arises less commonly at visceral sites. 23 Histologically, ASPS is classically characterized by epithelioid cells with a strikingly organoid/nested or pseudo-alveolar growth pattern surrounded by prominent vasculature. 24 These features may also be present in PEComa, although areas of discohesive growth are usually more focal.…”