Akrogerie vergesellschaftet mit progressiver Sklerodermie

Halter, K

doi:10.1007/bf02716900

Cited by 7 publications

(3 citation statements)

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“…Due to the missing subcutaneous fat 389 in the face and the thin, sharp nose the affected persons look older than they are. Mottled hyperpigmentation of the skin is found in one-third of the patients [7,9,11,14,15,17,18,19,20,24,25,31,33]. About 30% complain of increased bruising, which may be due to increased vulnerability of the vessels caused by the missing protection of the subcutis.…”

Section: Discussionmentioning

confidence: 99%

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Gottron's acrogeria and sarcoidosis

Meurer

Lohmöller²,

Keller³

1993

Clin Investig

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Section: Discussionmentioning

confidence: 99%

“…According to the literature, the main symptom of skeletal involvement is poor development of individual bones up to acromicria ( Table 2). The bone structure of six patients was described as osteoporotic [5,8,11,12,14,17]. Two other cases presented with acroosteolysis [9,19].…”

Section: Discussionmentioning

confidence: 99%

Gottron's acrogeria and sarcoidosis

Meurer

Lohmöller²,

Keller³

1993

Clin Investig

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“…Schwierigkeiten kann die Abgrenzung dieser lokalisierten Form eines Vergreisungssyndroms insbesondere von der progressiven systemischen Sklerodermie bereiten [5]. Auch die Konkordanz beider Erkrankungen ist bekannt [12].…”

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Metagerie - Klinisches Erscheinungsbild eines Vergreisungssyndroms

1997

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A 19-year old caucasian patient suffered from ulceration and scaring of his fingers since age two. During childhood, fibrosing contractures on the phalanges developed. Since puberty, his eunuch-like stature, bird-like face and exophthalmos had become under obvious. His hair was extraordinarily fine; his pubic hair rare. Radiological examination revealed ankylosis and osteoporosis of the phalanges and carpals. Angiography showed occlusion of multiple digital and interdigital arteries. Furthermore, a bilateral posterior cataract, restrictive respiratory disease, impaired glucose tolerance, hyperuricemia, proteinuria and primary hypogonadism were diagnosed. These findings are characteristic for the premature aging syndromes. The cardial symptoms of tall stature, bird-like face, pseudoexophthalmos, skleroderma-like and poikiloderma-like cutaneous lesions, scarce hair growth, early diabetes mellitus and arteriosclerosis led to the diagnosis of metageria.

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Fehlbildungen der Haut und Hautveränderungen bei Fehlbildungssyndromen

Korting

1963

Nicht Entzündliche Dermatosen I

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Akrogerie vergesellschaftet mit progressiver Sklerodermie

Cited by 7 publications

References 1 publication

Gottron's acrogeria and sarcoidosis

Gottron's acrogeria and sarcoidosis

Metagerie - Klinisches Erscheinungsbild eines Vergreisungssyndroms

Fehlbildungen der Haut und Hautveränderungen bei Fehlbildungssyndromen

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