Agminated fibroblastic connective tissue nevus in a 1‐year‐old boy

Abstract

Fibroblastic connective tissue nevus (FCTN) is a benign cutaneous mesenchymal lesion characterized by proliferation of CD34‐positive fibroblastic/myofibroblastic spindle‐shaped cells. We report a case of agminated FCTN on the right lower abdomen of a 1‐year‐old boy.

Progressive atrophic indurated plaques in a 16‐year‐old boy

“…Clinically, and similarly to connective tissue naevi, FCTN present as solitary, slow growing, painless, plaque-like or nodular lesions. 1,2 However, agminated variants 3,4 suggestive of sarcoma, lipoma and vascular malformation have also been reported. 5 Histologically, FCTN is characterized by a poorly defined proliferation of bland spindle cells with pale eosinophilic cytoplasm and tapering nuclei, arranged in randomly orientated short intersecting fascicles infiltrating the reticular dermis and the upper subcutis.…”

“…Clinically, and similarly to connective tissue naevi, FCTN present as solitary, slow growing, painless, plaque‐like or nodular lesions 1,2 . However, agminated variants 3,4 suggestive of sarcoma, lipoma and vascular malformation have also been reported 5 …”